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Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction
We report a case of surgical management of Crouzon syndrome with multisuture craniosynostosis presenting with increased intracranial pressure (ICP) manifesting with chronic papilledema without ventriculomegaly. A 12-month-old boy had complete resolution of papilledema after posterior cranial vault d...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5588654/ https://www.ncbi.nlm.nih.gov/pubmed/28904587 http://dx.doi.org/10.4103/jpn.JPN_15_17 |
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author | LoPresti, Melissa Buchanan, Edward P. Shah, Veeral Hadley, Caroline M. Monson, Laura A. Lam, Sandi |
author_facet | LoPresti, Melissa Buchanan, Edward P. Shah, Veeral Hadley, Caroline M. Monson, Laura A. Lam, Sandi |
author_sort | LoPresti, Melissa |
collection | PubMed |
description | We report a case of surgical management of Crouzon syndrome with multisuture craniosynostosis presenting with increased intracranial pressure (ICP) manifesting with chronic papilledema without ventriculomegaly. A 12-month-old boy had complete resolution of papilledema after posterior cranial vault distraction followed by staged fronto-orbital advancement. Expansion of the cranial vault with posterior distraction osteogenesis posed an elegant treatment, obviating ventriculoperitoneal shunt placement for cerebrospinal fluid (CSF) diversion. Strategies for the management of elevated ICP without ventriculomegaly in craniosynostosis include CSF shunting and cranial vault expansion. Posterior calvarial vault distraction associated with resolved papilledema has not been previously reported. Addressing the craniocephalic disproportion for this child with chronic papilledema, without ventriculomegaly, allowed the possibility of shunt freedom. |
format | Online Article Text |
id | pubmed-5588654 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-55886542017-09-13 Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction LoPresti, Melissa Buchanan, Edward P. Shah, Veeral Hadley, Caroline M. Monson, Laura A. Lam, Sandi J Pediatr Neurosci Case Report We report a case of surgical management of Crouzon syndrome with multisuture craniosynostosis presenting with increased intracranial pressure (ICP) manifesting with chronic papilledema without ventriculomegaly. A 12-month-old boy had complete resolution of papilledema after posterior cranial vault distraction followed by staged fronto-orbital advancement. Expansion of the cranial vault with posterior distraction osteogenesis posed an elegant treatment, obviating ventriculoperitoneal shunt placement for cerebrospinal fluid (CSF) diversion. Strategies for the management of elevated ICP without ventriculomegaly in craniosynostosis include CSF shunting and cranial vault expansion. Posterior calvarial vault distraction associated with resolved papilledema has not been previously reported. Addressing the craniocephalic disproportion for this child with chronic papilledema, without ventriculomegaly, allowed the possibility of shunt freedom. Medknow Publications & Media Pvt Ltd 2017 /pmc/articles/PMC5588654/ /pubmed/28904587 http://dx.doi.org/10.4103/jpn.JPN_15_17 Text en Copyright: © 2017 Journal of Pediatric Neurosciences http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Case Report LoPresti, Melissa Buchanan, Edward P. Shah, Veeral Hadley, Caroline M. Monson, Laura A. Lam, Sandi Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction |
title | Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction |
title_full | Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction |
title_fullStr | Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction |
title_full_unstemmed | Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction |
title_short | Complete Resolution of Papilledema in Syndromic Craniosynostosis with Posterior Cranial Vault Distraction |
title_sort | complete resolution of papilledema in syndromic craniosynostosis with posterior cranial vault distraction |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5588654/ https://www.ncbi.nlm.nih.gov/pubmed/28904587 http://dx.doi.org/10.4103/jpn.JPN_15_17 |
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