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Do you know this syndrome? Heerfordt-Waldenström syndrome

Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis and anterior uveitis. Granulomas with a peripheral lymphocyte deficit are found in the anatomic pathology of affected organs. It is normall...

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Autores principales: Fraga, Rafael Cavanellas, Kakizaki, Priscila, Valente, Neusa Yuriko Sakai, Portocarrero, Larissa Karine Leite, Teixeira, Mônica Fernandes Senise, Senise, Priscilla Fernandes
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5595615/
https://www.ncbi.nlm.nih.gov/pubmed/28954117
http://dx.doi.org/10.1590/abd1806-4841.20175211
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author Fraga, Rafael Cavanellas
Kakizaki, Priscila
Valente, Neusa Yuriko Sakai
Portocarrero, Larissa Karine Leite
Teixeira, Mônica Fernandes Senise
Senise, Priscilla Fernandes
author_facet Fraga, Rafael Cavanellas
Kakizaki, Priscila
Valente, Neusa Yuriko Sakai
Portocarrero, Larissa Karine Leite
Teixeira, Mônica Fernandes Senise
Senise, Priscilla Fernandes
author_sort Fraga, Rafael Cavanellas
collection PubMed
description Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis and anterior uveitis. Granulomas with a peripheral lymphocyte deficit are found in the anatomic pathology of affected organs. It is normally self-limiting, with cure achieved between 12 and 36 months, but some prolonged cases have been reported. Diagnosis of the syndrome is clinical, and treatment depends on the degree of systemic impairment. Oral corticosteroids represent the first line treatment option. The mortality rate ranges between 1 and 5% of cases.
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spelling pubmed-55956152017-09-19 Do you know this syndrome? Heerfordt-Waldenström syndrome Fraga, Rafael Cavanellas Kakizaki, Priscila Valente, Neusa Yuriko Sakai Portocarrero, Larissa Karine Leite Teixeira, Mônica Fernandes Senise Senise, Priscilla Fernandes An Bras Dermatol Syndrome in Question Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis and anterior uveitis. Granulomas with a peripheral lymphocyte deficit are found in the anatomic pathology of affected organs. It is normally self-limiting, with cure achieved between 12 and 36 months, but some prolonged cases have been reported. Diagnosis of the syndrome is clinical, and treatment depends on the degree of systemic impairment. Oral corticosteroids represent the first line treatment option. The mortality rate ranges between 1 and 5% of cases. Sociedade Brasileira de Dermatologia 2017 /pmc/articles/PMC5595615/ /pubmed/28954117 http://dx.doi.org/10.1590/abd1806-4841.20175211 Text en http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial No Derivative License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided the original work is properly cited and the work is not changed in any way.
spellingShingle Syndrome in Question
Fraga, Rafael Cavanellas
Kakizaki, Priscila
Valente, Neusa Yuriko Sakai
Portocarrero, Larissa Karine Leite
Teixeira, Mônica Fernandes Senise
Senise, Priscilla Fernandes
Do you know this syndrome? Heerfordt-Waldenström syndrome
title Do you know this syndrome? Heerfordt-Waldenström syndrome
title_full Do you know this syndrome? Heerfordt-Waldenström syndrome
title_fullStr Do you know this syndrome? Heerfordt-Waldenström syndrome
title_full_unstemmed Do you know this syndrome? Heerfordt-Waldenström syndrome
title_short Do you know this syndrome? Heerfordt-Waldenström syndrome
title_sort do you know this syndrome? heerfordt-waldenström syndrome
topic Syndrome in Question
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5595615/
https://www.ncbi.nlm.nih.gov/pubmed/28954117
http://dx.doi.org/10.1590/abd1806-4841.20175211
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