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Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor
INTRODUCTION: Solitary fibrous tumor is a rare type of mesenchymal, spindle-cell tumor reported mostly in the pleura. Retroperitoneal occurrence is rare and histopathological diagnosis is challenging. CASE PRESENTATION: A 55-year-old woman with nonspecific abdominal pain was found to have a retroper...
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5613361/ https://www.ncbi.nlm.nih.gov/pubmed/29138700 http://dx.doi.org/10.1155/2017/4634235 |
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author | Myoteri, D. Dellaportas, D. Nastos, C. Gioti, I. Gkiokas, G. Carvounis, E. Theodosopoulos, T. |
author_facet | Myoteri, D. Dellaportas, D. Nastos, C. Gioti, I. Gkiokas, G. Carvounis, E. Theodosopoulos, T. |
author_sort | Myoteri, D. |
collection | PubMed |
description | INTRODUCTION: Solitary fibrous tumor is a rare type of mesenchymal, spindle-cell tumor reported mostly in the pleura. Retroperitoneal occurrence is rare and histopathological diagnosis is challenging. CASE PRESENTATION: A 55-year-old woman with nonspecific abdominal pain was found to have a retroperitoneal/pelvic mass adjacent to the upper rectum. The patient underwent surgical resection in clear margins of this pelvic tumor, entering the total mesenteric excision surgical plane. Final histopathology revealed a solitary fibrous tumor and the case is presented herein. DISCUSSION: Solitary fibrous tumor in the retroperitoneum is rarely found in the literature and to the best of our knowledge less than a hundred cases are described so far. Histopathological diagnosis is mostly based on a “patternless pattern” on microscopic examination, which is a storiform arrangement of spindle cells combined with a “hemangiopericytoma-like appearance” and increased vascularity of the lesion. Surgery is the mainstay of treatment and recurrence rates are generally low. |
format | Online Article Text |
id | pubmed-5613361 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Hindawi |
record_format | MEDLINE/PubMed |
spelling | pubmed-56133612017-11-14 Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor Myoteri, D. Dellaportas, D. Nastos, C. Gioti, I. Gkiokas, G. Carvounis, E. Theodosopoulos, T. Case Rep Oncol Med Case Report INTRODUCTION: Solitary fibrous tumor is a rare type of mesenchymal, spindle-cell tumor reported mostly in the pleura. Retroperitoneal occurrence is rare and histopathological diagnosis is challenging. CASE PRESENTATION: A 55-year-old woman with nonspecific abdominal pain was found to have a retroperitoneal/pelvic mass adjacent to the upper rectum. The patient underwent surgical resection in clear margins of this pelvic tumor, entering the total mesenteric excision surgical plane. Final histopathology revealed a solitary fibrous tumor and the case is presented herein. DISCUSSION: Solitary fibrous tumor in the retroperitoneum is rarely found in the literature and to the best of our knowledge less than a hundred cases are described so far. Histopathological diagnosis is mostly based on a “patternless pattern” on microscopic examination, which is a storiform arrangement of spindle cells combined with a “hemangiopericytoma-like appearance” and increased vascularity of the lesion. Surgery is the mainstay of treatment and recurrence rates are generally low. Hindawi 2017 2017-09-12 /pmc/articles/PMC5613361/ /pubmed/29138700 http://dx.doi.org/10.1155/2017/4634235 Text en Copyright © 2017 D. Myoteri et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Myoteri, D. Dellaportas, D. Nastos, C. Gioti, I. Gkiokas, G. Carvounis, E. Theodosopoulos, T. Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor |
title | Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor |
title_full | Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor |
title_fullStr | Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor |
title_full_unstemmed | Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor |
title_short | Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor |
title_sort | retroperitoneal solitary fibrous tumor: a “patternless” tumor |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5613361/ https://www.ncbi.nlm.nih.gov/pubmed/29138700 http://dx.doi.org/10.1155/2017/4634235 |
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