Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1

Benign and malignant tumors are common in the setting of neurofibromatosis type 1 (NF1). Malignant peripheral nerve sheath tumor (MPNST) and angiosarcoma are rare tumors in children and adolescents and mostly occur in young patients in relation to NF1. Both histological types can be present in the s...

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Autores principales: Milković Periša, Marija, Džombeta, Tihana, Stepan Giljević, Jasminka, Krušlin, Božo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2017
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5613689/
https://www.ncbi.nlm.nih.gov/pubmed/29138703
http://dx.doi.org/10.1155/2017/7542825
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author Milković Periša, Marija
Džombeta, Tihana
Stepan Giljević, Jasminka
Krušlin, Božo
author_facet Milković Periša, Marija
Džombeta, Tihana
Stepan Giljević, Jasminka
Krušlin, Božo
author_sort Milković Periša, Marija
collection PubMed
description Benign and malignant tumors are common in the setting of neurofibromatosis type 1 (NF1). Malignant peripheral nerve sheath tumor (MPNST) and angiosarcoma are rare tumors in children and adolescents and mostly occur in young patients in relation to NF1. Both histological types can be present in the same tumor mass in patients with NF1. We present a case of 12.5-year-old girl with NF1 who first presented with MPNST of the right inguinal region and 1.5 years later with unrelated angiosarcoma of the scalp.
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spelling pubmed-56136892017-11-14 Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1 Milković Periša, Marija Džombeta, Tihana Stepan Giljević, Jasminka Krušlin, Božo Case Rep Pathol Case Report Benign and malignant tumors are common in the setting of neurofibromatosis type 1 (NF1). Malignant peripheral nerve sheath tumor (MPNST) and angiosarcoma are rare tumors in children and adolescents and mostly occur in young patients in relation to NF1. Both histological types can be present in the same tumor mass in patients with NF1. We present a case of 12.5-year-old girl with NF1 who first presented with MPNST of the right inguinal region and 1.5 years later with unrelated angiosarcoma of the scalp. Hindawi 2017 2017-08-24 /pmc/articles/PMC5613689/ /pubmed/29138703 http://dx.doi.org/10.1155/2017/7542825 Text en Copyright © 2017 Marija Milković Periša et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Milković Periša, Marija
Džombeta, Tihana
Stepan Giljević, Jasminka
Krušlin, Božo
Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1
title Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1
title_full Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1
title_fullStr Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1
title_full_unstemmed Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1
title_short Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1
title_sort malignant peripheral nerve sheath tumor of the inguinum and angiosarcoma of the scalp in a child with neurofibromatosis type 1
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5613689/
https://www.ncbi.nlm.nih.gov/pubmed/29138703
http://dx.doi.org/10.1155/2017/7542825
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