Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature

Dermatofibrosarcoma protuberans is a soft tissue sarcoma that is dermal in origin. The incidence is <0.1% of all malignancies and 1% of soft tissue sarcoma. Most commonly, it involves trunk (62%) followed by extremities (25%) and head and neck (13%). It is a slow growing tumor with locally aggres...

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Autores principales: Sharma, Deepti, Singh, Garima, Kakkar, Neha, Jha, Vidya
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Brief Communications
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5621282/
https://www.ncbi.nlm.nih.gov/pubmed/28905843
http://dx.doi.org/10.4103/ijo.IJO_770_16
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author Sharma, Deepti
Singh, Garima
Kakkar, Neha
Jha, Vidya
author_facet Sharma, Deepti
Singh, Garima
Kakkar, Neha
Jha, Vidya
author_sort Sharma, Deepti
collection PubMed
description Dermatofibrosarcoma protuberans is a soft tissue sarcoma that is dermal in origin. The incidence is <0.1% of all malignancies and 1% of soft tissue sarcoma. Most commonly, it involves trunk (62%) followed by extremities (25%) and head and neck (13%). It is a slow growing tumor with locally aggressive behavior. Here, a 50-year-old female diagnosed with orbital dermatofibrosarcoma developed extra-axial component in right frontal region even on chemotherapy. Hence, the bad prognostic factors are yet to be established in dermatofibrosarcoma protuberans.
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spelling pubmed-56212822017-10-04 Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature Sharma, Deepti Singh, Garima Kakkar, Neha Jha, Vidya Indian J Ophthalmol Brief Communications Dermatofibrosarcoma protuberans is a soft tissue sarcoma that is dermal in origin. The incidence is <0.1% of all malignancies and 1% of soft tissue sarcoma. Most commonly, it involves trunk (62%) followed by extremities (25%) and head and neck (13%). It is a slow growing tumor with locally aggressive behavior. Here, a 50-year-old female diagnosed with orbital dermatofibrosarcoma developed extra-axial component in right frontal region even on chemotherapy. Hence, the bad prognostic factors are yet to be established in dermatofibrosarcoma protuberans. Medknow Publications & Media Pvt Ltd 2017-09 /pmc/articles/PMC5621282/ /pubmed/28905843 http://dx.doi.org/10.4103/ijo.IJO_770_16 Text en Copyright: © 2017 Indian Journal of Ophthalmology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Brief Communications
Sharma, Deepti
Singh, Garima
Kakkar, Neha
Jha, Vidya
Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature
title Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature
title_full Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature
title_fullStr Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature
title_full_unstemmed Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature
title_short Orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: A case report and brief review of literature
title_sort orbital dermatofibrosarcoma protuberans with frontal and ethmoid sinus involvement: a case report and brief review of literature
topic Brief Communications
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5621282/
https://www.ncbi.nlm.nih.gov/pubmed/28905843
http://dx.doi.org/10.4103/ijo.IJO_770_16
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