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Pulmonary hypertension subtypes associated with hereditary haemorrhagic telangiectasia: Haemodynamic profiles and survival probability

BACKGROUND: Different pulmonary hypertension (PH) mechanisms are associated with hereditary haemorrhagic telangiectasia (HHT). METHODS AND RESULTS: We conducted a retrospective study of all suspected cases of PH (echocardiographically estimated systolic pulmonary artery pressure [sPAP] ≥ 40 mmHg) in...

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Detalles Bibliográficos
Autores principales:	Revuz, Sabine, Decullier, Evelyne, Ginon, Isabelle, Lamblin, Nicolas, Hatron, Pierre-Yves, Kaminsky, Pierre, Carette, Marie-France, Lacombe, Pascal, Simon, Anne-Claire, Rivière, Sophie, Harlé, Jean-Robert, Fraisse, Alain, Lavigne, Christian, Leguy-Seguin, Vanessa, Chaouat, Ari, Khouatra, Chahera, Dupuis-Girod, Sophie, Hachulla, Eric
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2017
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5628806/ https://www.ncbi.nlm.nih.gov/pubmed/28981519 http://dx.doi.org/10.1371/journal.pone.0184227

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