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Saline is as effective as nitrogen scavengers for treatment of hyperammonemia

Urea cycle enzyme deficiency (UCED) patients with hyperammonemia are treated with sodium benzoate (SB) and sodium phenylacetate (SPA) to induce alternative pathways of nitrogen excretion. The suggested guidelines supporting their use in the management of hyperammonemia are primarily based on non-ana...

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Detalles Bibliográficos
Autores principales:	van Straten, G., de Sain-van der Velden, M. G. M., van Geijlswijk, I. M., Favier, R. P., Mesu, S. J., Holwerda-Loof, N. E., van der Ham, M., Fieten, H., Rothuizen, J., Spee, B., Verhoeven-Duif, N. M.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Nature Publishing Group UK 2017
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5640627/ https://www.ncbi.nlm.nih.gov/pubmed/29030642 http://dx.doi.org/10.1038/s41598-017-12686-9

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