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Congenital hepatic fibrosis in a 9-year-old female patient – a case report

Congenital hepatic fibrosis (CHF) is a rare, autosomal recessive disorder, clinically characterized by hepatic fibrosis and portal hypertension. CHF results from ductal plate malformation (DPM) of the intrahepatic bile ducts. Four clinical forms can be observed: portal hypertensive, cholangitic, mix...

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Detalles Bibliográficos
Autores principales:	Janowski, Kamil, Goliszek, Maria, Cielecka-Kuszyk, Joanna, Jankowska, Irena, Pawłowska, Joanna
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Termedia Publishing House 2017
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5649488/ https://www.ncbi.nlm.nih.gov/pubmed/29062909 http://dx.doi.org/10.5114/ceh.2017.70299

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