Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report

Sclerosing epithelioid fibrosarcoma (SEF) is a rare and aggressive tumor for which no standardized treatment regimens are available. The occurrence of this tumor in children and adolescents has been rarely reported, especially in the head and neck region. Involvement of the neuraxis is reported only...

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Autores principales: Kilaikode, Sasikumar, Kuril, Sandeepkumar, Sedrak, Aziza, Sadanandan, Swayam
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elmer Press 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5649852/
https://www.ncbi.nlm.nih.gov/pubmed/29147367
http://dx.doi.org/10.4021/wjon742w
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author Kilaikode, Sasikumar
Kuril, Sandeepkumar
Sedrak, Aziza
Sadanandan, Swayam
author_facet Kilaikode, Sasikumar
Kuril, Sandeepkumar
Sedrak, Aziza
Sadanandan, Swayam
author_sort Kilaikode, Sasikumar
collection PubMed
description Sclerosing epithelioid fibrosarcoma (SEF) is a rare and aggressive tumor for which no standardized treatment regimens are available. The occurrence of this tumor in children and adolescents has been rarely reported, especially in the head and neck region. Involvement of the neuraxis is reported only in a few patients. We report a case of a 13-year-old boy with SEF of the skull with intracranial extension. The tumor recurred after initial resection and rapidly spread to the brain parenchyma and the meninges with no response to surgery, chemotherapy and radiation therapy.
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spelling pubmed-56498522017-11-16 Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report Kilaikode, Sasikumar Kuril, Sandeepkumar Sedrak, Aziza Sadanandan, Swayam World J Oncol Case Report Sclerosing epithelioid fibrosarcoma (SEF) is a rare and aggressive tumor for which no standardized treatment regimens are available. The occurrence of this tumor in children and adolescents has been rarely reported, especially in the head and neck region. Involvement of the neuraxis is reported only in a few patients. We report a case of a 13-year-old boy with SEF of the skull with intracranial extension. The tumor recurred after initial resection and rapidly spread to the brain parenchyma and the meninges with no response to surgery, chemotherapy and radiation therapy. Elmer Press 2013-12 2014-01-16 /pmc/articles/PMC5649852/ /pubmed/29147367 http://dx.doi.org/10.4021/wjon742w Text en Copyright 2013, Kilaikode et al. http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Kilaikode, Sasikumar
Kuril, Sandeepkumar
Sedrak, Aziza
Sadanandan, Swayam
Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report
title Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report
title_full Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report
title_fullStr Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report
title_full_unstemmed Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report
title_short Sclerosing Epithelioid Fibrosarcoma of the Parietal Bone and Adjacent Meninges in an Adolescent: A Case Report
title_sort sclerosing epithelioid fibrosarcoma of the parietal bone and adjacent meninges in an adolescent: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5649852/
https://www.ncbi.nlm.nih.gov/pubmed/29147367
http://dx.doi.org/10.4021/wjon742w
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