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Dietary management of maternal phenylketonuria with glycomacropeptide and amino acids supplements: A case report

BACKGROUND: In maternal PKU, protein substitute (PS) is provided by phenylalanine (PHE)-free l-amino acids (AA), but glycomacropeptide-based protein substitute (GMP) is an alternative consideration. OBJECTIVE: To describe the first Portuguese Maternal Phenylketonuria (MPKU) partially managed with GM...

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Detalles Bibliográficos
Autores principales:	Pinto, A., Almeida, M.F., Cunha, A., Carmona, C., Rocha, S., Guimas, A., Ribeiro, R., Mota, C.R., Martins, E., MacDonald, A., Rocha, J.C.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elsevier 2017
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5650649/ https://www.ncbi.nlm.nih.gov/pubmed/29085781 http://dx.doi.org/10.1016/j.ymgmr.2017.10.004

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