Oral administration of pyrophosphate inhibits connective tissue calcification

Various disorders including pseudoxanthoma elasticum (PXE) and generalized arterial calcification of infancy (GACI), which are caused by inactivating mutations in ABCC6 and ENPP1, respectively, present with extensive tissue calcification due to reduced plasma pyrophosphate (PPi). However, it has alw...

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Detalles Bibliográficos
Autores principales: Dedinszki, Dóra, Szeri, Flóra, Kozák, Eszter, Pomozi, Viola, Tőkési, Natália, Mezei, Tamás Róbert, Merczel, Kinga, Letavernier, Emmanuel, Tang, Ellie, Le Saux, Olivier, Arányi, Tamás, van de Wetering, Koen, Váradi, András
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2017
Materias:
Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5666306/
https://www.ncbi.nlm.nih.gov/pubmed/28701330
http://dx.doi.org/10.15252/emmm.201707532

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