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Outcomes of long term treatments of type I hereditary angioedema in a Turkish family

BACKGROUND: Hereditary angioedema is a rare autosomal dominantly inherited immunodeficiency disorder characterized by potentially life-threatening angioedema attacks. OBJECTIVE: We aimed to investigate the clinical and genetic features of a family with angioedema attacks. METHODS: The medical histor...

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Detalles Bibliográficos
Autores principales: Akoglu, Gulsen, Kesim, Belgin, Yildiz, Gokhan, Metin, Ahmet
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5674698/
https://www.ncbi.nlm.nih.gov/pubmed/29166502
http://dx.doi.org/10.1590/abd1806-4841.20175899