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Negative Staining for COL4A5 Correlates With Worse Prognosis and More Severe Ultrastructural Alterations in Males With Alport Syndrome

INTRODUCTION: Alport syndrome (AS) is a genetic disorder characterized by progressive hematuric nephropathy with or without sensorineural hearing loss and ocular lesions. Previous studies on AS included mostly children. METHODS: To determine the prognostic value of loss of staining for collagen type...

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Detalles Bibliográficos
Autores principales:	Said, Samar M., Fidler, Mary E., Valeri, Anthony M., McCann, Brooke, Fiedler, Wade, Cornell, Lynn D., Alexander, Mariam Priya, Alkhunaizi, Ahmed M., Sullivan, Anne, Cramer, Carl H., Hogan, Marie C., Nasr, Samih H.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elsevier 2016
Materias:	Clinical Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5678677/ https://www.ncbi.nlm.nih.gov/pubmed/29142939 http://dx.doi.org/10.1016/j.ekir.2016.09.056

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