Unusual case of hemangioblastoma of the cerebellopontine angle

BACKGROUND: Hemangioblastomas are the most common primary tumor of the posterior fossa. There are few cases of hemangioblastoma of the cerebellopontine angle (CPA). When present in this location, hemangioblastoma presents a diagnostic challenge as its imaging findings closely resemble those of vestibular schwannoma (VS), which is much more common in the CPA. CASE DESCRIPTION: We report the case of a 42-year-old man presenting with vertigo and diplopia found to have a CPA tumor with imaging resembling VS. He underwent retrosigmoidal resection of his tumor, which was found to be a hemangioblastoma. CONCLUSION: Hemangioblastoma, though rare in the CPA, should be considered in the differential diagnosis of CPA tumors.