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Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case

Rhabdoid tumor commonly occurs in the kidney and has an aggressive clinical course with high mortality. Central nervous system is the most common extrarenal site. Extrarenal extracranial rhabdoid tumor (EERT) is rare. EERT usually presents in childhood, and presentation in adulthood is extremely rar...

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Detalles Bibliográficos
Autores principales: Devnani, Bharti, Biswas, Ahitagni, Bakhshi, Sameer, Kaushal, Seema, Nakra, Tripti
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5686991/
https://www.ncbi.nlm.nih.gov/pubmed/29200698
http://dx.doi.org/10.4103/ijmpo.ijmpo_108_17
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author Devnani, Bharti
Biswas, Ahitagni
Bakhshi, Sameer
Kaushal, Seema
Nakra, Tripti
author_facet Devnani, Bharti
Biswas, Ahitagni
Bakhshi, Sameer
Kaushal, Seema
Nakra, Tripti
author_sort Devnani, Bharti
collection PubMed
description Rhabdoid tumor commonly occurs in the kidney and has an aggressive clinical course with high mortality. Central nervous system is the most common extrarenal site. Extrarenal extracranial rhabdoid tumor (EERT) is rare. EERT usually presents in childhood, and presentation in adulthood is extremely rare. This tumor is often difficult to diagnose, and there is no established standard of care due to the paucity of cases. We herein report a case of extrarenal rhabdoid tumor of the pelvis in a young adult and discuss the presentation and possible treatment options of this rare tumor.
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spelling pubmed-56869912017-12-01 Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case Devnani, Bharti Biswas, Ahitagni Bakhshi, Sameer Kaushal, Seema Nakra, Tripti Indian J Med Paediatr Oncol Case Report Rhabdoid tumor commonly occurs in the kidney and has an aggressive clinical course with high mortality. Central nervous system is the most common extrarenal site. Extrarenal extracranial rhabdoid tumor (EERT) is rare. EERT usually presents in childhood, and presentation in adulthood is extremely rare. This tumor is often difficult to diagnose, and there is no established standard of care due to the paucity of cases. We herein report a case of extrarenal rhabdoid tumor of the pelvis in a young adult and discuss the presentation and possible treatment options of this rare tumor. Medknow Publications & Media Pvt Ltd 2017 /pmc/articles/PMC5686991/ /pubmed/29200698 http://dx.doi.org/10.4103/ijmpo.ijmpo_108_17 Text en Copyright: © 2017 Indian Journal of Medical and Paediatric Oncology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Devnani, Bharti
Biswas, Ahitagni
Bakhshi, Sameer
Kaushal, Seema
Nakra, Tripti
Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case
title Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case
title_full Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case
title_fullStr Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case
title_full_unstemmed Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case
title_short Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult-management of a Challenging Case
title_sort extrarenal extracranial rhabdoid tumor of the pelvis in a young adult-management of a challenging case
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5686991/
https://www.ncbi.nlm.nih.gov/pubmed/29200698
http://dx.doi.org/10.4103/ijmpo.ijmpo_108_17
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