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Brazilian guidelines for the diagnosis and treatment of cystic fibrosis

Cystic fibrosis (CF) is an autosomal recessive genetic disorder characterized by dysfunction of the CFTR gene. It is a multisystem disease that most often affects White individuals. In recent decades, various advances in the diagnosis and treatment of CF have drastically changed the scenario, result...

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Detalles Bibliográficos
Autores principales:	Athanazio, Rodrigo Abensur, da Silva, Luiz Vicente Ribeiro Ferreira, Vergara, Alberto Andrade, Ribeiro, Antônio Fernando, Riedi, Carlos Antônio, Procianoy, Elenara da Fonseca Andrade, Adde, Fabíola Villac, Reis, Francisco José Caldeira, Ribeiro, José Dirceu, Torres, Lídia Alice, de Fuccio, Marcelo Bicalho, Epifanio, Matias, Firmida, Mônica de Cássia, Damaceno, Neiva, Ludwig-Neto, Norberto, Maróstica, Paulo José Cauduro, Rached, Samia Zahi, Melo, Suzana Fonseca de Oliveira
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Sociedade Brasileira de Pneumologia e Tisiologia 2017
Materias:	Special Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5687954/ https://www.ncbi.nlm.nih.gov/pubmed/28746534 http://dx.doi.org/10.1590/S1806-37562017000000065

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