Isolated hepatoblastoma arising from the hepatogastric ligament: a case report

BACKGROUND: Almost all hepatoblastomas are isolated to the liver. Hepatoblastoma arising from and limited to extrahepatic tissue is an extremely rare clinical entity. CASE PRESENTATION: Here we present a case of a 7-year-old Chinese boy of Han ethnicity with hepatoblastoma originating from the hepat...

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Autores principales: Chen, Ji, Sun, Mengjiao, Sun, Bin, Yi, Jun, Jiang, Bin, Huang, Lei
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2017
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5697092/
https://www.ncbi.nlm.nih.gov/pubmed/29157294
http://dx.doi.org/10.1186/s13256-017-1488-8
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author Chen, Ji
Sun, Mengjiao
Sun, Bin
Yi, Jun
Jiang, Bin
Huang, Lei
author_facet Chen, Ji
Sun, Mengjiao
Sun, Bin
Yi, Jun
Jiang, Bin
Huang, Lei
author_sort Chen, Ji
collection PubMed
description BACKGROUND: Almost all hepatoblastomas are isolated to the liver. Hepatoblastoma arising from and limited to extrahepatic tissue is an extremely rare clinical entity. CASE PRESENTATION: Here we present a case of a 7-year-old Chinese boy of Han ethnicity with hepatoblastoma originating from the hepatogastric ligament. A complete resection was performed and the entire course was uneventful. He received six cycles of postoperative chemotherapy and had no signs of recurrence for 3 years after surgery. CONCLUSIONS: Hepatoblastoma arising from extrahepatic tissue is extremely rare. A pedunculated hepatoblastoma is prone to hemorrhage and tumor metastasis. The best treatment for a long-term cure is complete resection of the primary tumor combined with chemotherapy.
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spelling pubmed-56970922017-12-01 Isolated hepatoblastoma arising from the hepatogastric ligament: a case report Chen, Ji Sun, Mengjiao Sun, Bin Yi, Jun Jiang, Bin Huang, Lei J Med Case Rep Case Report BACKGROUND: Almost all hepatoblastomas are isolated to the liver. Hepatoblastoma arising from and limited to extrahepatic tissue is an extremely rare clinical entity. CASE PRESENTATION: Here we present a case of a 7-year-old Chinese boy of Han ethnicity with hepatoblastoma originating from the hepatogastric ligament. A complete resection was performed and the entire course was uneventful. He received six cycles of postoperative chemotherapy and had no signs of recurrence for 3 years after surgery. CONCLUSIONS: Hepatoblastoma arising from extrahepatic tissue is extremely rare. A pedunculated hepatoblastoma is prone to hemorrhage and tumor metastasis. The best treatment for a long-term cure is complete resection of the primary tumor combined with chemotherapy. BioMed Central 2017-11-21 /pmc/articles/PMC5697092/ /pubmed/29157294 http://dx.doi.org/10.1186/s13256-017-1488-8 Text en © The Author(s). 2017 Open AccessThis article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Chen, Ji
Sun, Mengjiao
Sun, Bin
Yi, Jun
Jiang, Bin
Huang, Lei
Isolated hepatoblastoma arising from the hepatogastric ligament: a case report
title Isolated hepatoblastoma arising from the hepatogastric ligament: a case report
title_full Isolated hepatoblastoma arising from the hepatogastric ligament: a case report
title_fullStr Isolated hepatoblastoma arising from the hepatogastric ligament: a case report
title_full_unstemmed Isolated hepatoblastoma arising from the hepatogastric ligament: a case report
title_short Isolated hepatoblastoma arising from the hepatogastric ligament: a case report
title_sort isolated hepatoblastoma arising from the hepatogastric ligament: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5697092/
https://www.ncbi.nlm.nih.gov/pubmed/29157294
http://dx.doi.org/10.1186/s13256-017-1488-8
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