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Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles?

Nearly 50 years after the pioneering procedure performed by Francis Fontan and Eugene Baudet, which has saved the lives of thousands of children, there are still more questions than answers regarding therapeutic management. The complex pathophysiology of Fontan circulation, the lack of clear guideli...

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Detalles Bibliográficos
Autores principales: Cześniewicz, Paweł J., Kusa, Jacek
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Termedia Publishing House 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5701595/
https://www.ncbi.nlm.nih.gov/pubmed/29181047
http://dx.doi.org/10.5114/kitp.2017.70533
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author Cześniewicz, Paweł J.
Kusa, Jacek
author_facet Cześniewicz, Paweł J.
Kusa, Jacek
author_sort Cześniewicz, Paweł J.
collection PubMed
description Nearly 50 years after the pioneering procedure performed by Francis Fontan and Eugene Baudet, which has saved the lives of thousands of children, there are still more questions than answers regarding therapeutic management. The complex pathophysiology of Fontan circulation, the lack of clear guidelines, and the shift in the care of such patients from pediatric cardiological and cardiac surgical centers to ones dealing with adult patients, cause new threats. This paper outlines the fundamental issues related to the pathophysiology of Fontan circulation and reviews the literature on the methods of treating complications characteristic of this group of patients.
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spelling pubmed-57015952017-11-27 Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles? Cześniewicz, Paweł J. Kusa, Jacek Kardiochir Torakochirurgia Pol Review Paper Nearly 50 years after the pioneering procedure performed by Francis Fontan and Eugene Baudet, which has saved the lives of thousands of children, there are still more questions than answers regarding therapeutic management. The complex pathophysiology of Fontan circulation, the lack of clear guidelines, and the shift in the care of such patients from pediatric cardiological and cardiac surgical centers to ones dealing with adult patients, cause new threats. This paper outlines the fundamental issues related to the pathophysiology of Fontan circulation and reviews the literature on the methods of treating complications characteristic of this group of patients. Termedia Publishing House 2017-09-30 2017-09 /pmc/articles/PMC5701595/ /pubmed/29181047 http://dx.doi.org/10.5114/kitp.2017.70533 Text en Copyright: © 2017 Polish Society of Cardiothoracic Surgeons (Polskie Towarzystwo KardioTorakochirurgów) and the editors of the Polish Journal of Cardio-Thoracic Surgery (Kardiochirurgia i Torakochirurgia Polska) http://creativecommons.org/licenses/by-nc-sa/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) License, allowing third parties to copy and redistribute the material in any medium or format and to remix, transform, and build upon the material, provided the original work is properly cited and states its license.
spellingShingle Review Paper
Cześniewicz, Paweł J.
Kusa, Jacek
Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles?
title Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles?
title_full Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles?
title_fullStr Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles?
title_full_unstemmed Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles?
title_short Approaching the 50(th) anniversary of the first Fontan procedure. What is the current state of treatment provided to patients with functional single ventricles?
title_sort approaching the 50(th) anniversary of the first fontan procedure. what is the current state of treatment provided to patients with functional single ventricles?
topic Review Paper
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5701595/
https://www.ncbi.nlm.nih.gov/pubmed/29181047
http://dx.doi.org/10.5114/kitp.2017.70533
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