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Bacterial infections in patients with primary ciliary dyskinesia: Comparison with cystic fibrosis
Primary ciliary dyskinesia (PCD) is an autosomal recessive disorder associated with severely impaired mucociliary clearance caused by defects in ciliary structure and function. Although recurrent bacterial infection of the respiratory tract is one of the major clinical features of this disease, PCD...
Autores principales: | Wijers, Christiaan DM, Chmiel, James F, Gaston, Benjamin M |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
SAGE Publications
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5729729/ https://www.ncbi.nlm.nih.gov/pubmed/29081265 http://dx.doi.org/10.1177/1479972317694621 |
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