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A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia

Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunu...

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Detalles Bibliográficos
Autores principales: Ottenhoff, Janna S.E., Nikkels, Peter G.J., Terwisscha van Scheltinga, C.E.J., Naeije, L.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5731177/
https://www.ncbi.nlm.nih.gov/pubmed/29279689
http://dx.doi.org/10.1159/000481305
Descripción
Sumario:Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunum, and totally resected. In case of a solitary lesion, treatment is relatively easy and effective, with excellent prognosis after total resection. The multiple form (myofibromatosis) has a poor prognosis with low survival rates. We therefore recommend total body MRI for all patients diagnosed with myofibroma to rule out other lesions.