Cargando…
A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia
Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunu...
Autores principales: | , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
S. Karger AG
2017
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5731177/ https://www.ncbi.nlm.nih.gov/pubmed/29279689 http://dx.doi.org/10.1159/000481305 |
_version_ | 1783286478482178048 |
---|---|
author | Ottenhoff, Janna S.E. Nikkels, Peter G.J. Terwisscha van Scheltinga, C.E.J. Naeije, L. |
author_facet | Ottenhoff, Janna S.E. Nikkels, Peter G.J. Terwisscha van Scheltinga, C.E.J. Naeije, L. |
author_sort | Ottenhoff, Janna S.E. |
collection | PubMed |
description | Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunum, and totally resected. In case of a solitary lesion, treatment is relatively easy and effective, with excellent prognosis after total resection. The multiple form (myofibromatosis) has a poor prognosis with low survival rates. We therefore recommend total body MRI for all patients diagnosed with myofibroma to rule out other lesions. |
format | Online Article Text |
id | pubmed-5731177 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | S. Karger AG |
record_format | MEDLINE/PubMed |
spelling | pubmed-57311772017-12-26 A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia Ottenhoff, Janna S.E. Nikkels, Peter G.J. Terwisscha van Scheltinga, C.E.J. Naeije, L. Case Rep Oncol Case Report Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunum, and totally resected. In case of a solitary lesion, treatment is relatively easy and effective, with excellent prognosis after total resection. The multiple form (myofibromatosis) has a poor prognosis with low survival rates. We therefore recommend total body MRI for all patients diagnosed with myofibroma to rule out other lesions. S. Karger AG 2017-10-17 /pmc/articles/PMC5731177/ /pubmed/29279689 http://dx.doi.org/10.1159/000481305 Text en Copyright © 2017 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/4.0/ This article is licensed under the Creative Commons Attribution-NonCommercial-4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission. |
spellingShingle | Case Report Ottenhoff, Janna S.E. Nikkels, Peter G.J. Terwisscha van Scheltinga, C.E.J. Naeije, L. A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia |
title | A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia |
title_full | A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia |
title_fullStr | A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia |
title_full_unstemmed | A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia |
title_short | A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia |
title_sort | solitary intestinal myofibroma: a rare cause of neonatal anemia |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5731177/ https://www.ncbi.nlm.nih.gov/pubmed/29279689 http://dx.doi.org/10.1159/000481305 |
work_keys_str_mv | AT ottenhoffjannase asolitaryintestinalmyofibromaararecauseofneonatalanemia AT nikkelspetergj asolitaryintestinalmyofibromaararecauseofneonatalanemia AT terwisschavanscheltingacej asolitaryintestinalmyofibromaararecauseofneonatalanemia AT naeijel asolitaryintestinalmyofibromaararecauseofneonatalanemia AT ottenhoffjannase solitaryintestinalmyofibromaararecauseofneonatalanemia AT nikkelspetergj solitaryintestinalmyofibromaararecauseofneonatalanemia AT terwisschavanscheltingacej solitaryintestinalmyofibromaararecauseofneonatalanemia AT naeijel solitaryintestinalmyofibromaararecauseofneonatalanemia |