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A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia

Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunu...

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Autores principales: Ottenhoff, Janna S.E., Nikkels, Peter G.J., Terwisscha van Scheltinga, C.E.J., Naeije, L.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5731177/
https://www.ncbi.nlm.nih.gov/pubmed/29279689
http://dx.doi.org/10.1159/000481305
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author Ottenhoff, Janna S.E.
Nikkels, Peter G.J.
Terwisscha van Scheltinga, C.E.J.
Naeije, L.
author_facet Ottenhoff, Janna S.E.
Nikkels, Peter G.J.
Terwisscha van Scheltinga, C.E.J.
Naeije, L.
author_sort Ottenhoff, Janna S.E.
collection PubMed
description Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunum, and totally resected. In case of a solitary lesion, treatment is relatively easy and effective, with excellent prognosis after total resection. The multiple form (myofibromatosis) has a poor prognosis with low survival rates. We therefore recommend total body MRI for all patients diagnosed with myofibroma to rule out other lesions.
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spelling pubmed-57311772017-12-26 A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia Ottenhoff, Janna S.E. Nikkels, Peter G.J. Terwisscha van Scheltinga, C.E.J. Naeije, L. Case Rep Oncol Case Report Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunum, and totally resected. In case of a solitary lesion, treatment is relatively easy and effective, with excellent prognosis after total resection. The multiple form (myofibromatosis) has a poor prognosis with low survival rates. We therefore recommend total body MRI for all patients diagnosed with myofibroma to rule out other lesions. S. Karger AG 2017-10-17 /pmc/articles/PMC5731177/ /pubmed/29279689 http://dx.doi.org/10.1159/000481305 Text en Copyright © 2017 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/4.0/ This article is licensed under the Creative Commons Attribution-NonCommercial-4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission.
spellingShingle Case Report
Ottenhoff, Janna S.E.
Nikkels, Peter G.J.
Terwisscha van Scheltinga, C.E.J.
Naeije, L.
A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia
title A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia
title_full A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia
title_fullStr A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia
title_full_unstemmed A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia
title_short A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia
title_sort solitary intestinal myofibroma: a rare cause of neonatal anemia
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5731177/
https://www.ncbi.nlm.nih.gov/pubmed/29279689
http://dx.doi.org/10.1159/000481305
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