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Unusual Straatsma Syndrome - How dogmatic is a bad prognosis?

PURPOSE: To show that Straatsma Syndrome can have a good outcome and to highlight an unusual presentation of this disease. OBSERVATIONS: A four-year-old boy presents with severe right eye amblyopia in association with high myopia, esotropia, heterochromia iridum and extensive myelinated retinal fibe...

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Detalles Bibliográficos
Autores principales: Vide-Escada, Ana, Prior Filipe, Helena
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5731674/
https://www.ncbi.nlm.nih.gov/pubmed/29260122
http://dx.doi.org/10.1016/j.ajoc.2017.10.003

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