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Refractory ventricular fibrillations after surgical repair of atrial septal defects in a patient with CACNA1C gene mutation - case report

BACKGROUND: Congenital long QT syndrome (LQTS) can cause ventricular arrhythmic events with syncope and sudden death resulting from malignant torsades de pointes (TdP) followed by ventricular fibrillations (VFs). However, the syndrome is often overlooked prior to the development of arrhythmic events...

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Detalles Bibliográficos
Autores principales:	Kojima, Ai, Shikata, Fumiaki, Okamura, Toru, Higaki, Takashi, Ohno, Seiko, Horie, Minoru, Uchita, Shunji, Kawanishi, Yujiro, Namiguchi, Kenji, Yasugi, Takumi, Izutani, Hironori
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2017
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5735880/ https://www.ncbi.nlm.nih.gov/pubmed/29258620 http://dx.doi.org/10.1186/s13019-017-0683-4

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