Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression

Langerhans cell histiocytosis (LCH) is a disorder of the monocyte-macrophage system that can be unifocal or systemic. Here, we present a pediatric case who initially presented with osseous LCH but again presented 6 years later emergently with cerebellar symptoms, cerebellar mass and obstructive hydr...

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Autores principales: Rajderkar, Dhanashree A, Shah, Mrunal L, Shah, Jehan L
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Paediatric
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5761170/
https://www.ncbi.nlm.nih.gov/pubmed/29379238
http://dx.doi.org/10.4103/ijri.IJRI_389_16
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author Rajderkar, Dhanashree A
Shah, Mrunal L
Shah, Jehan L
author_facet Rajderkar, Dhanashree A
Shah, Mrunal L
Shah, Jehan L
author_sort Rajderkar, Dhanashree A
collection PubMed
description Langerhans cell histiocytosis (LCH) is a disorder of the monocyte-macrophage system that can be unifocal or systemic. Here, we present a pediatric case who initially presented with osseous LCH but again presented 6 years later emergently with cerebellar symptoms, cerebellar mass and obstructive hydrocephalus. Patient underwent biopsy of the cerebellum which was path proven intracranial LCH.
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spelling pubmed-57611702018-01-29 Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression Rajderkar, Dhanashree A Shah, Mrunal L Shah, Jehan L Indian J Radiol Imaging Paediatric Langerhans cell histiocytosis (LCH) is a disorder of the monocyte-macrophage system that can be unifocal or systemic. Here, we present a pediatric case who initially presented with osseous LCH but again presented 6 years later emergently with cerebellar symptoms, cerebellar mass and obstructive hydrocephalus. Patient underwent biopsy of the cerebellum which was path proven intracranial LCH. Medknow Publications & Media Pvt Ltd 2017 /pmc/articles/PMC5761170/ /pubmed/29379238 http://dx.doi.org/10.4103/ijri.IJRI_389_16 Text en Copyright: © 2017 Indian Journal of Radiology and Imaging http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Paediatric
Rajderkar, Dhanashree A
Shah, Mrunal L
Shah, Jehan L
Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression
title Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression
title_full Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression
title_fullStr Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression
title_full_unstemmed Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression
title_short Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression
title_sort emergent presentation of langerhans cell histiocytosis in a pediatric patient: acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression
topic Paediatric
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5761170/
https://www.ncbi.nlm.nih.gov/pubmed/29379238
http://dx.doi.org/10.4103/ijri.IJRI_389_16
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