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Severe Loss of Tritan Color Discrimination in RPE65 Associated Leber Congenital Amaurosis
PURPOSE: RPE65-associated Leber congenital amaurosis (RPE65-LCA) is a progressive severe retinal dystrophy with early profound dysfunction of rod photoreceptors followed by progressive cone photoreceptor degeneration. We aim to provide detailed information about how cone dysfunction affects color di...
Autores principales: | Kumaran, Neruban, Ripamonti, Caterina, Kalitzeos, Angelos, Rubin, Gary S., Bainbridge, James W. B., Michaelides, Michel |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Association for Research in Vision and Ophthalmology
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5769497/ https://www.ncbi.nlm.nih.gov/pubmed/29332120 http://dx.doi.org/10.1167/iovs.17-22905 |
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