Surgical management for a huge presacral teratoma and a meningocele in an adult with Currarino triad: a case report

BACKGROUND: The Currarino triad is a rare hereditary syndrome comprising anorectal malformation, sacral bony defect, and presacral mass. Most of the patients are diagnosed during infancy. CASE PRESENTATION: A 44-year-old man was diagnosed with Currarino triad, with a huge presacral teratoma and meni...

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Detalles Bibliográficos
Autores principales: Emoto, Shigenobu, Kaneko, Manabu, Murono, Koji, Sasaki, Kazuhito, Otani, Kensuke, Nishikawa, Takeshi, Tanaka, Toshiaki, Hata, Keisuke, Kawai, Kazushige, Imai, Hideaki, Saito, Nobuhito, Kobayashi, Hiroshi, Tanaka, Sakae, Ikemura, Masako, Ushiku, Tetsuo, Nozawa, Hiroaki
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer Berlin Heidelberg 2018
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5775187/
https://www.ncbi.nlm.nih.gov/pubmed/29352751
http://dx.doi.org/10.1186/s40792-018-0419-2
Descripción
Sumario:BACKGROUND: The Currarino triad is a rare hereditary syndrome comprising anorectal malformation, sacral bony defect, and presacral mass. Most of the patients are diagnosed during infancy. CASE PRESENTATION: A 44-year-old man was diagnosed with Currarino triad, with a huge presacral teratoma and meningocele. One-stage surgery via posterior approach was successful. CONCLUSIONS: Treatment of the presacral mass in the Currarino triad, diagnosed in adulthood, is challenging. Multidisciplinary management and detailed planning before surgery are important for a satisfactory outcome.

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