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Inherited thrombotic thrombocytopenic purpura mimicking immune thrombocytopenic purpura during pregnancy: a case report

BACKGROUND: Thrombotic thrombocytopenic purpura is a very rare hereditary blood deficiency disorder of ADAMTS13 (von Willebrand factor-cleaving protease) and a life-threatening thrombotic microangiopathy characterized by thrombocytopenia and microangiopathic hemolytic anemia. The deficiency in ADAMT...

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Detalles Bibliográficos
Autores principales: Romão de Souza, Valter, Beatriz Cavalcante de Oliveira, Ana, Maria Vanderlei, Ana, Queiroz da Mota Silveira Aroucha, Amanda, Pontes Duarte, Bruna, Nunes Machado, Aureli, Netto Chaer, Lívia, Wanderley de Barros Correia, Cláudia, da Conceição de Barros Correia, Maria, Freire Hazin Costa, Manuela
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5778757/
https://www.ncbi.nlm.nih.gov/pubmed/29357939
http://dx.doi.org/10.1186/s13256-017-1545-3