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Inherited thrombotic thrombocytopenic purpura mimicking immune thrombocytopenic purpura during pregnancy: a case report
BACKGROUND: Thrombotic thrombocytopenic purpura is a very rare hereditary blood deficiency disorder of ADAMTS13 (von Willebrand factor-cleaving protease) and a life-threatening thrombotic microangiopathy characterized by thrombocytopenia and microangiopathic hemolytic anemia. The deficiency in ADAMT...
Autores principales: | Romão de Souza, Valter, Beatriz Cavalcante de Oliveira, Ana, Maria Vanderlei, Ana, Queiroz da Mota Silveira Aroucha, Amanda, Pontes Duarte, Bruna, Nunes Machado, Aureli, Netto Chaer, Lívia, Wanderley de Barros Correia, Cláudia, da Conceição de Barros Correia, Maria, Freire Hazin Costa, Manuela |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5778757/ https://www.ncbi.nlm.nih.gov/pubmed/29357939 http://dx.doi.org/10.1186/s13256-017-1545-3 |
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