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Infantile myofibromatosis

Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastin...

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Autores principales: Larralde, Margarita, Ferrari, Bruno, Martinez, Juan Pablo, Barbieri, María Angélica Fernández, Méndez, José Higinio, Casas, José
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5786406/
https://www.ncbi.nlm.nih.gov/pubmed/29364448
http://dx.doi.org/10.1590/abd1806-4841.20175001
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author Larralde, Margarita
Ferrari, Bruno
Martinez, Juan Pablo
Barbieri, María Angélica Fernández
Méndez, José Higinio
Casas, José
author_facet Larralde, Margarita
Ferrari, Bruno
Martinez, Juan Pablo
Barbieri, María Angélica Fernández
Méndez, José Higinio
Casas, José
author_sort Larralde, Margarita
collection PubMed
description Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed.
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spelling pubmed-57864062018-02-01 Infantile myofibromatosis Larralde, Margarita Ferrari, Bruno Martinez, Juan Pablo Barbieri, María Angélica Fernández Méndez, José Higinio Casas, José An Bras Dermatol Case Report Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed. Sociedade Brasileira de Dermatologia 2017 /pmc/articles/PMC5786406/ /pubmed/29364448 http://dx.doi.org/10.1590/abd1806-4841.20175001 Text en http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial No Derivative License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided the original work is properly cited and the work is not changed in any way.
spellingShingle Case Report
Larralde, Margarita
Ferrari, Bruno
Martinez, Juan Pablo
Barbieri, María Angélica Fernández
Méndez, José Higinio
Casas, José
Infantile myofibromatosis
title Infantile myofibromatosis
title_full Infantile myofibromatosis
title_fullStr Infantile myofibromatosis
title_full_unstemmed Infantile myofibromatosis
title_short Infantile myofibromatosis
title_sort infantile myofibromatosis
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5786406/
https://www.ncbi.nlm.nih.gov/pubmed/29364448
http://dx.doi.org/10.1590/abd1806-4841.20175001
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