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Infantile myofibromatosis
Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastin...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Sociedade Brasileira de Dermatologia
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5786406/ https://www.ncbi.nlm.nih.gov/pubmed/29364448 http://dx.doi.org/10.1590/abd1806-4841.20175001 |
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author | Larralde, Margarita Ferrari, Bruno Martinez, Juan Pablo Barbieri, María Angélica Fernández Méndez, José Higinio Casas, José |
author_facet | Larralde, Margarita Ferrari, Bruno Martinez, Juan Pablo Barbieri, María Angélica Fernández Méndez, José Higinio Casas, José |
author_sort | Larralde, Margarita |
collection | PubMed |
description | Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed. |
format | Online Article Text |
id | pubmed-5786406 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Sociedade Brasileira de Dermatologia |
record_format | MEDLINE/PubMed |
spelling | pubmed-57864062018-02-01 Infantile myofibromatosis Larralde, Margarita Ferrari, Bruno Martinez, Juan Pablo Barbieri, María Angélica Fernández Méndez, José Higinio Casas, José An Bras Dermatol Case Report Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed. Sociedade Brasileira de Dermatologia 2017 /pmc/articles/PMC5786406/ /pubmed/29364448 http://dx.doi.org/10.1590/abd1806-4841.20175001 Text en http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial No Derivative License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided the original work is properly cited and the work is not changed in any way. |
spellingShingle | Case Report Larralde, Margarita Ferrari, Bruno Martinez, Juan Pablo Barbieri, María Angélica Fernández Méndez, José Higinio Casas, José Infantile myofibromatosis |
title | Infantile myofibromatosis |
title_full | Infantile myofibromatosis |
title_fullStr | Infantile myofibromatosis |
title_full_unstemmed | Infantile myofibromatosis |
title_short | Infantile myofibromatosis |
title_sort | infantile myofibromatosis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5786406/ https://www.ncbi.nlm.nih.gov/pubmed/29364448 http://dx.doi.org/10.1590/abd1806-4841.20175001 |
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