Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy

Relapsing polychondritis (RP) is a rare systemic autoimmune disease that affects cartilaginous structures. RP causes tracheobronchomalacia (TBM) by affecting the bronchial cartilage. TBM is a fatal condition characterized by excessive weakening of the walls of the trachea and bronchi. We herein repo...

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Autores principales: Oryoji, Daisuke, Ono, Nobuyuki, Himeji, Daisuke, Yoshihiro, Kyoko, Kai, Yasufumi, Matsuda, Motohiro, Tsukamoto, Hiroshi, Ueda, Akira
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Japanese Society of Internal Medicine 2017
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5790730/
https://www.ncbi.nlm.nih.gov/pubmed/29021454
http://dx.doi.org/10.2169/internalmedicine.8778-16
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author Oryoji, Daisuke
Ono, Nobuyuki
Himeji, Daisuke
Yoshihiro, Kyoko
Kai, Yasufumi
Matsuda, Motohiro
Tsukamoto, Hiroshi
Ueda, Akira
author_facet Oryoji, Daisuke
Ono, Nobuyuki
Himeji, Daisuke
Yoshihiro, Kyoko
Kai, Yasufumi
Matsuda, Motohiro
Tsukamoto, Hiroshi
Ueda, Akira
author_sort Oryoji, Daisuke
collection PubMed
description Relapsing polychondritis (RP) is a rare systemic autoimmune disease that affects cartilaginous structures. RP causes tracheobronchomalacia (TBM) by affecting the bronchial cartilage. TBM is a fatal condition characterized by excessive weakening of the walls of the trachea and bronchi. We herein report a case of a 73-year-old man who experienced sudden respiratory failure due to TBM caused by RP. Immunosuppressive treatment did not improve his respiratory failure. Multiple metallic stentings dramatically improved his severe airway symptoms. When the airway condition becomes lethal in RP patients, then metallic stenting can be a useful treatment option.
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spelling pubmed-57907302018-01-31 Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy Oryoji, Daisuke Ono, Nobuyuki Himeji, Daisuke Yoshihiro, Kyoko Kai, Yasufumi Matsuda, Motohiro Tsukamoto, Hiroshi Ueda, Akira Intern Med Case Report Relapsing polychondritis (RP) is a rare systemic autoimmune disease that affects cartilaginous structures. RP causes tracheobronchomalacia (TBM) by affecting the bronchial cartilage. TBM is a fatal condition characterized by excessive weakening of the walls of the trachea and bronchi. We herein report a case of a 73-year-old man who experienced sudden respiratory failure due to TBM caused by RP. Immunosuppressive treatment did not improve his respiratory failure. Multiple metallic stentings dramatically improved his severe airway symptoms. When the airway condition becomes lethal in RP patients, then metallic stenting can be a useful treatment option. The Japanese Society of Internal Medicine 2017-10-11 2017-12-15 /pmc/articles/PMC5790730/ /pubmed/29021454 http://dx.doi.org/10.2169/internalmedicine.8778-16 Text en Copyright © 2017 by The Japanese Society of Internal Medicine https://creativecommons.org/licenses/by-nc-nd/4.0/ The Internal Medicine is an Open Access article distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Oryoji, Daisuke
Ono, Nobuyuki
Himeji, Daisuke
Yoshihiro, Kyoko
Kai, Yasufumi
Matsuda, Motohiro
Tsukamoto, Hiroshi
Ueda, Akira
Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy
title Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy
title_full Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy
title_fullStr Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy
title_full_unstemmed Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy
title_short Sudden Respiratory Failure due to Tracheobronchomalacia by Relapsing Polychondritis, Successfully Rescued by Multiple Metallic Stenting and Tracheostomy
title_sort sudden respiratory failure due to tracheobronchomalacia by relapsing polychondritis, successfully rescued by multiple metallic stenting and tracheostomy
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5790730/
https://www.ncbi.nlm.nih.gov/pubmed/29021454
http://dx.doi.org/10.2169/internalmedicine.8778-16
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