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Basement Membrane Defects in Genetic Kidney Diseases

The glomerular basement membrane (GBM) is a specialized structure with a significant role in maintaining the glomerular filtration barrier. This GBM is formed from the fusion of two basement membranes during development and its function in the filtration barrier is achieved by key extracellular matr...

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Detalles Bibliográficos
Autores principales:	Chew, Christine, Lennon, Rachel
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2018
Materias:	Pediatrics
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5796894/ https://www.ncbi.nlm.nih.gov/pubmed/29435440 http://dx.doi.org/10.3389/fped.2018.00011

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