Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti

Incontinentia pigmenti (IP) is a rare X-linked dominant disease that affects the ectodermal tissues. It is associated with a whorled pattern of scarring alopecia, which is possibly underreported. This scarring alopecia could be used as a marker to identify adult women affected with IP as older patie...

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Detalles Bibliográficos
Autores principales: Popli, Urvi, Yesudian, Paul Devakar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2018
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5803848/
https://www.ncbi.nlm.nih.gov/pubmed/29440854
http://dx.doi.org/10.4103/ijt.ijt_73_17
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author Popli, Urvi
Yesudian, Paul Devakar
author_facet Popli, Urvi
Yesudian, Paul Devakar
author_sort Popli, Urvi
collection PubMed
description Incontinentia pigmenti (IP) is a rare X-linked dominant disease that affects the ectodermal tissues. It is associated with a whorled pattern of scarring alopecia, which is possibly underreported. This scarring alopecia could be used as a marker to identify adult women affected with IP as older patients may have minimal cutaneous manifestations. We report an unusual case of an 8-year-old girl who had recurrent inflammatory stage IP and later developed whorled scarring alopecia in the vertex of the scalp.
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spelling pubmed-58038482018-02-13 Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti Popli, Urvi Yesudian, Paul Devakar Int J Trichology Case Report Incontinentia pigmenti (IP) is a rare X-linked dominant disease that affects the ectodermal tissues. It is associated with a whorled pattern of scarring alopecia, which is possibly underreported. This scarring alopecia could be used as a marker to identify adult women affected with IP as older patients may have minimal cutaneous manifestations. We report an unusual case of an 8-year-old girl who had recurrent inflammatory stage IP and later developed whorled scarring alopecia in the vertex of the scalp. Medknow Publications & Media Pvt Ltd 2018 /pmc/articles/PMC5803848/ /pubmed/29440854 http://dx.doi.org/10.4103/ijt.ijt_73_17 Text en Copyright: © 2018 International Journal of Trichology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution NonCommercial ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Popli, Urvi
Yesudian, Paul Devakar
Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti
title Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti
title_full Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti
title_fullStr Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti
title_full_unstemmed Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti
title_short Whorled Scarring Alopecia – The Only Adult Marker of Incontinentia Pigmenti
title_sort whorled scarring alopecia – the only adult marker of incontinentia pigmenti
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5803848/
https://www.ncbi.nlm.nih.gov/pubmed/29440854
http://dx.doi.org/10.4103/ijt.ijt_73_17
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