Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease

Acquired cutis laxa (ACL) is a rare connective tissue disorder characterized by pendulous and coarsely wrinkled skin. There have been few cases of its association to monoclonal immunoglobulin deposition disease (MIDD), which constitutes the light chain (LCDD), heavy chain (HCDD), and light and heavy...

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Detalles Bibliográficos
Autores principales: Majithia, Reena A., George, Leni, Thomas, Meera, Fouzia, N. A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2018
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5803942/
https://www.ncbi.nlm.nih.gov/pubmed/29441298
http://dx.doi.org/10.4103/idoj.IDOJ_403_16
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author Majithia, Reena A.
George, Leni
Thomas, Meera
Fouzia, N. A.
author_facet Majithia, Reena A.
George, Leni
Thomas, Meera
Fouzia, N. A.
author_sort Majithia, Reena A.
collection PubMed
description Acquired cutis laxa (ACL) is a rare connective tissue disorder characterized by pendulous and coarsely wrinkled skin. There have been few cases of its association to monoclonal immunoglobulin deposition disease (MIDD), which constitutes the light chain (LCDD), heavy chain (HCDD), and light and heavy chain (LHCDD) deposition disease. MIDD predominantly involves the kidney. Skin is the next common organ to be affected by HCDD, which presents as ACL. We report the case of a 40-year-old male who presented with ACL associated with LHCDD. The clinical features of ACL in the present case appeared prior to the development of clinical features related to LHCDD.
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spelling pubmed-58039422018-02-13 Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease Majithia, Reena A. George, Leni Thomas, Meera Fouzia, N. A. Indian Dermatol Online J Case Report Acquired cutis laxa (ACL) is a rare connective tissue disorder characterized by pendulous and coarsely wrinkled skin. There have been few cases of its association to monoclonal immunoglobulin deposition disease (MIDD), which constitutes the light chain (LCDD), heavy chain (HCDD), and light and heavy chain (LHCDD) deposition disease. MIDD predominantly involves the kidney. Skin is the next common organ to be affected by HCDD, which presents as ACL. We report the case of a 40-year-old male who presented with ACL associated with LHCDD. The clinical features of ACL in the present case appeared prior to the development of clinical features related to LHCDD. Medknow Publications & Media Pvt Ltd 2018 /pmc/articles/PMC5803942/ /pubmed/29441298 http://dx.doi.org/10.4103/idoj.IDOJ_403_16 Text en Copyright: © 2018 Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Majithia, Reena A.
George, Leni
Thomas, Meera
Fouzia, N. A.
Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease
title Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease
title_full Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease
title_fullStr Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease
title_full_unstemmed Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease
title_short Acquired Cutis Laxa Associated with Light and Heavy Chain Deposition Disease
title_sort acquired cutis laxa associated with light and heavy chain deposition disease
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5803942/
https://www.ncbi.nlm.nih.gov/pubmed/29441298
http://dx.doi.org/10.4103/idoj.IDOJ_403_16
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AT thomasmeera acquiredcutislaxaassociatedwithlightandheavychaindepositiondisease
AT fouziana acquiredcutislaxaassociatedwithlightandheavychaindepositiondisease

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