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Humanizing the mdx mouse model of DMD: the long and the short of it

Duchenne muscular dystrophy (DMD) is a common fatal heritable myopathy, with cardiorespiratory failure occurring by the third decade of life. There is no specific treatment for DMD cardiomyopathy, in large part due to a lack of understanding of the mechanisms underlying the cardiac failure. Mdx mice...

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Detalles Bibliográficos
Autores principales:	Yucel, Nora, Chang, Alex C., Day, John W., Rosenthal, Nadia, Blau, Helen M.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Nature Publishing Group UK 2018
Materias:	Review Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5816599/ https://www.ncbi.nlm.nih.gov/pubmed/29479480 http://dx.doi.org/10.1038/s41536-018-0045-4

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