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Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach

Ellis-van Creveld syndrome (EVC) is a very rare genetic disorder that affects various tissues of ectodermal and mesodermal origin; patients with EVC present with typical oral deficiencies. The affected individuals are quite young at the time of oral evaluation. It is, therefore, important that these...

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Detalles Bibliográficos
Autores principales: Naqash, Talib Amin, Alshahrani, Ibrahim, Simasetha, Siripan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5828096/
https://www.ncbi.nlm.nih.gov/pubmed/29607224
http://dx.doi.org/10.1155/2018/8631602
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author Naqash, Talib Amin
Alshahrani, Ibrahim
Simasetha, Siripan
author_facet Naqash, Talib Amin
Alshahrani, Ibrahim
Simasetha, Siripan
author_sort Naqash, Talib Amin
collection PubMed
description Ellis-van Creveld syndrome (EVC) is a very rare genetic disorder that affects various tissues of ectodermal and mesodermal origin; patients with EVC present with typical oral deficiencies. The affected individuals are quite young at the time of oral evaluation. It is, therefore, important that these individuals are diagnosed and receive dental treatment at an early age for their physiologic and psychosocial well-being. Albeit there are numerous articles penned on the EVC, the treatise from an oral perspective is inadequate, covering only oral exhibitions and the preventive treatments. This article reviews the literature and serves as the first disquisition for oral rehabilitation of an EVC patient utilizing surgical, orthodontic, restorative, and prosthodontic management.
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spelling pubmed-58280962018-04-01 Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach Naqash, Talib Amin Alshahrani, Ibrahim Simasetha, Siripan Case Rep Dent Case Report Ellis-van Creveld syndrome (EVC) is a very rare genetic disorder that affects various tissues of ectodermal and mesodermal origin; patients with EVC present with typical oral deficiencies. The affected individuals are quite young at the time of oral evaluation. It is, therefore, important that these individuals are diagnosed and receive dental treatment at an early age for their physiologic and psychosocial well-being. Albeit there are numerous articles penned on the EVC, the treatise from an oral perspective is inadequate, covering only oral exhibitions and the preventive treatments. This article reviews the literature and serves as the first disquisition for oral rehabilitation of an EVC patient utilizing surgical, orthodontic, restorative, and prosthodontic management. Hindawi 2018-01-23 /pmc/articles/PMC5828096/ /pubmed/29607224 http://dx.doi.org/10.1155/2018/8631602 Text en Copyright © 2018 Talib Amin Naqash et al. http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Naqash, Talib Amin
Alshahrani, Ibrahim
Simasetha, Siripan
Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_full Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_fullStr Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_full_unstemmed Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_short Ellis-van Creveld Syndrome: A Rare Clinical Report of Oral Rehabilitation by Interdisciplinary Approach
title_sort ellis-van creveld syndrome: a rare clinical report of oral rehabilitation by interdisciplinary approach
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5828096/
https://www.ncbi.nlm.nih.gov/pubmed/29607224
http://dx.doi.org/10.1155/2018/8631602
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