Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome

We report the case of a young woman with hereditary hemorrhagic telangiectasia (HHT) with severe liver involvement and pulmonary shunting. The medical imaging in this patient illustrates the severe shunting that can occur in these patients who often are asymptomatic. By showing this case, we want to...

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Autores principales: Verhelst, Xavier, Geerts, Anja, Van Vlierberghe, Hans, Smeets, Peter, Lecluyse, Clarisse
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2018
Materias:
Single Case
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5836288/
https://www.ncbi.nlm.nih.gov/pubmed/29515340
http://dx.doi.org/10.1159/000486189
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author Verhelst, Xavier
Geerts, Anja
Van Vlierberghe, Hans
Smeets, Peter
Lecluyse, Clarisse
author_facet Verhelst, Xavier
Geerts, Anja
Van Vlierberghe, Hans
Smeets, Peter
Lecluyse, Clarisse
author_sort Verhelst, Xavier
collection PubMed
description We report the case of a young woman with hereditary hemorrhagic telangiectasia (HHT) with severe liver involvement and pulmonary shunting. The medical imaging in this patient illustrates the severe shunting that can occur in these patients who often are asymptomatic. By showing this case, we want to highlight the role of liver transplantation in HHT with hepatic involvement.
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spelling pubmed-58362882018-03-07 Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome Verhelst, Xavier Geerts, Anja Van Vlierberghe, Hans Smeets, Peter Lecluyse, Clarisse Case Rep Gastroenterol Single Case We report the case of a young woman with hereditary hemorrhagic telangiectasia (HHT) with severe liver involvement and pulmonary shunting. The medical imaging in this patient illustrates the severe shunting that can occur in these patients who often are asymptomatic. By showing this case, we want to highlight the role of liver transplantation in HHT with hepatic involvement. S. Karger AG 2018-01-17 /pmc/articles/PMC5836288/ /pubmed/29515340 http://dx.doi.org/10.1159/000486189 Text en Copyright © 2018 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/4.0/ This article is licensed under the Creative Commons Attribution-NonCommercial-4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission.
spellingShingle Single Case
Verhelst, Xavier
Geerts, Anja
Van Vlierberghe, Hans
Smeets, Peter
Lecluyse, Clarisse
Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_full Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_fullStr Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_full_unstemmed Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_short Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_sort severe hepatic and pulmonary involvement in rendu-osler-weber syndrome
topic Single Case
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5836288/
https://www.ncbi.nlm.nih.gov/pubmed/29515340
http://dx.doi.org/10.1159/000486189
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