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The histopathology and phenotypic variability in H syndrome

Skin biopsy may be helpful in the diagnosis of H syndrome. A triad of dermal fibrosis, lymphocytic aggregates, and numerous CD68+, CD163+, S100‐positive, and CD1a‐negative dermal histiocytes is characteristic.

Detalles Bibliográficos
Autores principales: Dias‐Polak, David, Indelman, Margarita, Bergman, Reuven, Avitan‐Hersh, Emily
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5838267/
https://www.ncbi.nlm.nih.gov/pubmed/29531721
http://dx.doi.org/10.1002/ccr3.1329
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author Dias‐Polak, David
Indelman, Margarita
Bergman, Reuven
Avitan‐Hersh, Emily
author_facet Dias‐Polak, David
Indelman, Margarita
Bergman, Reuven
Avitan‐Hersh, Emily
author_sort Dias‐Polak, David
collection PubMed
description Skin biopsy may be helpful in the diagnosis of H syndrome. A triad of dermal fibrosis, lymphocytic aggregates, and numerous CD68+, CD163+, S100‐positive, and CD1a‐negative dermal histiocytes is characteristic.
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spelling pubmed-58382672018-03-12 The histopathology and phenotypic variability in H syndrome Dias‐Polak, David Indelman, Margarita Bergman, Reuven Avitan‐Hersh, Emily Clin Case Rep Case Reports Skin biopsy may be helpful in the diagnosis of H syndrome. A triad of dermal fibrosis, lymphocytic aggregates, and numerous CD68+, CD163+, S100‐positive, and CD1a‐negative dermal histiocytes is characteristic. John Wiley and Sons Inc. 2018-01-25 /pmc/articles/PMC5838267/ /pubmed/29531721 http://dx.doi.org/10.1002/ccr3.1329 Text en © 2018 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the Creative Commons Attribution (http://creativecommons.org/licenses/by/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Dias‐Polak, David
Indelman, Margarita
Bergman, Reuven
Avitan‐Hersh, Emily
The histopathology and phenotypic variability in H syndrome
title The histopathology and phenotypic variability in H syndrome
title_full The histopathology and phenotypic variability in H syndrome
title_fullStr The histopathology and phenotypic variability in H syndrome
title_full_unstemmed The histopathology and phenotypic variability in H syndrome
title_short The histopathology and phenotypic variability in H syndrome
title_sort histopathology and phenotypic variability in h syndrome
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5838267/
https://www.ncbi.nlm.nih.gov/pubmed/29531721
http://dx.doi.org/10.1002/ccr3.1329
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