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Primary Ciliary Dyskinesia Due to Microtubular Defects is Associated with Worse Lung Clearance Index
PURPOSE: Primary ciliary dyskinesia (PCD) is characterised by repeated upper and lower respiratory tract infections, neutrophilic airway inflammation and obstructive airway disease. Different ultrastructural ciliary defects may affect lung function decline to different degrees. Lung clearance index...
Autores principales: | Irving, S., Dixon, M., Fassad, M. R., Frost, E., Hayward, J., Kilpin, K., Ollosson, S., Onoufriadis, A., Patel, M. P., Scully, J., Carr, S. B., Mitchison, H. M., Loebinger, M. R., Hogg, C., Shoemark, A., Bush, A. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Springer US
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5854730/ https://www.ncbi.nlm.nih.gov/pubmed/29368042 http://dx.doi.org/10.1007/s00408-018-0086-x |
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