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Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who...
Autores principales: | , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5865522/ https://www.ncbi.nlm.nih.gov/pubmed/29593876 http://dx.doi.org/10.1093/omcr/omx108 |
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author | Alicea-Guevara, Ricardo Cruz Caliz, Michael Adorno, Jose Fernandez, Ricardo Rivera, Kelvin Gonzalez, Gustavo Hernandez-Castillo, Ricardo Alan Fernandez, Rosangela Castillo Latorre, Christian |
author_facet | Alicea-Guevara, Ricardo Cruz Caliz, Michael Adorno, Jose Fernandez, Ricardo Rivera, Kelvin Gonzalez, Gustavo Hernandez-Castillo, Ricardo Alan Fernandez, Rosangela Castillo Latorre, Christian |
author_sort | Alicea-Guevara, Ricardo |
collection | PubMed |
description | Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding. |
format | Online Article Text |
id | pubmed-5865522 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-58655222018-03-28 Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome Alicea-Guevara, Ricardo Cruz Caliz, Michael Adorno, Jose Fernandez, Ricardo Rivera, Kelvin Gonzalez, Gustavo Hernandez-Castillo, Ricardo Alan Fernandez, Rosangela Castillo Latorre, Christian Oxf Med Case Reports Case Report Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding. Oxford University Press 2018-03-22 /pmc/articles/PMC5865522/ /pubmed/29593876 http://dx.doi.org/10.1093/omcr/omx108 Text en © The Author(s) 2018. Published by Oxford University Press. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com |
spellingShingle | Case Report Alicea-Guevara, Ricardo Cruz Caliz, Michael Adorno, Jose Fernandez, Ricardo Rivera, Kelvin Gonzalez, Gustavo Hernandez-Castillo, Ricardo Alan Fernandez, Rosangela Castillo Latorre, Christian Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome |
title | Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome |
title_full | Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome |
title_fullStr | Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome |
title_full_unstemmed | Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome |
title_short | Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome |
title_sort | life-threatening hemoptysis: case of osler–weber–rendu syndrome |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5865522/ https://www.ncbi.nlm.nih.gov/pubmed/29593876 http://dx.doi.org/10.1093/omcr/omx108 |
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