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Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome

Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who...

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Autores principales: Alicea-Guevara, Ricardo, Cruz Caliz, Michael, Adorno, Jose, Fernandez, Ricardo, Rivera, Kelvin, Gonzalez, Gustavo, Hernandez-Castillo, Ricardo Alan, Fernandez, Rosangela, Castillo Latorre, Christian
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5865522/
https://www.ncbi.nlm.nih.gov/pubmed/29593876
http://dx.doi.org/10.1093/omcr/omx108
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author Alicea-Guevara, Ricardo
Cruz Caliz, Michael
Adorno, Jose
Fernandez, Ricardo
Rivera, Kelvin
Gonzalez, Gustavo
Hernandez-Castillo, Ricardo Alan
Fernandez, Rosangela
Castillo Latorre, Christian
author_facet Alicea-Guevara, Ricardo
Cruz Caliz, Michael
Adorno, Jose
Fernandez, Ricardo
Rivera, Kelvin
Gonzalez, Gustavo
Hernandez-Castillo, Ricardo Alan
Fernandez, Rosangela
Castillo Latorre, Christian
author_sort Alicea-Guevara, Ricardo
collection PubMed
description Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding.
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spelling pubmed-58655222018-03-28 Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome Alicea-Guevara, Ricardo Cruz Caliz, Michael Adorno, Jose Fernandez, Ricardo Rivera, Kelvin Gonzalez, Gustavo Hernandez-Castillo, Ricardo Alan Fernandez, Rosangela Castillo Latorre, Christian Oxf Med Case Reports Case Report Hereditary haemorrhagic telangiectasia (HHT), also known as Osler–Weber–Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding. Oxford University Press 2018-03-22 /pmc/articles/PMC5865522/ /pubmed/29593876 http://dx.doi.org/10.1093/omcr/omx108 Text en © The Author(s) 2018. Published by Oxford University Press. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
Alicea-Guevara, Ricardo
Cruz Caliz, Michael
Adorno, Jose
Fernandez, Ricardo
Rivera, Kelvin
Gonzalez, Gustavo
Hernandez-Castillo, Ricardo Alan
Fernandez, Rosangela
Castillo Latorre, Christian
Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
title Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
title_full Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
title_fullStr Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
title_full_unstemmed Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
title_short Life-threatening hemoptysis: case of Osler–Weber–Rendu Syndrome
title_sort life-threatening hemoptysis: case of osler–weber–rendu syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5865522/
https://www.ncbi.nlm.nih.gov/pubmed/29593876
http://dx.doi.org/10.1093/omcr/omx108
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