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Long-term evolution of lung function in individuals with alpha-1 antitrypsin deficiency from the Spanish registry (REDAAT)
BACKGROUND: The clinical course of alpha-1 antitrypsin deficiency (AATD) is very heterogeneous. It is estimated that 60% of individuals with severe AATD (Pi*ZZ) develop emphysema. The main objective of this study was to describe the outcomes of long-term lung function in individuals with AATD-associ...
Autores principales: | Esquinas, Cristina, Serreri, Sonia, Barrecheguren, Miriam, Rodriguez, Esther, Nuñez, Alexa, Casas-Maldonado, Francisco, Blanco, Ignacio, Pirina, Pietro, Lara, Beatriz, Miravitlles, Marc |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Dove Medical Press
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5870637/ https://www.ncbi.nlm.nih.gov/pubmed/29615836 http://dx.doi.org/10.2147/COPD.S155226 |
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