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A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma
Cardiac angiosarcomas are extremely rare in childhood, they are rapidly progressive tumours that often present themselves as diagnostic dilemmas, resulting in delayed diagnosis. Also, extracardiac manifestations, including abdominal pain, are extremely rare in patients with intracardiac tumors. We h...
Autores principales: | , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Sociedade Brasileira de Cirurgia Cardiovascular
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5873788/ https://www.ncbi.nlm.nih.gov/pubmed/29617509 http://dx.doi.org/10.21470/1678-9741-2017-0095 |
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author | Citak, Elvan Caglar Ozeren, Murat Karaca, M. Kerem Karpuz, Derya Karahan, Feryal Yilmaz, Eda Bengi Balci, Yuksel Kara, Pelin Ozcan Arpaci, Rabia Bozdogan |
author_facet | Citak, Elvan Caglar Ozeren, Murat Karaca, M. Kerem Karpuz, Derya Karahan, Feryal Yilmaz, Eda Bengi Balci, Yuksel Kara, Pelin Ozcan Arpaci, Rabia Bozdogan |
author_sort | Citak, Elvan Caglar |
collection | PubMed |
description | Cardiac angiosarcomas are extremely rare in childhood, they are rapidly progressive tumours that often present themselves as diagnostic dilemmas, resulting in delayed diagnosis. Also, extracardiac manifestations, including abdominal pain, are extremely rare in patients with intracardiac tumors. We herein present the case of a 15-year-old girl who presented with abdominal pain. Echocardiography and thoracic computed tomography showed right atrial mass. The patient underwent surgery, chemotherapy, and radiotherapy. Eight months after treatment, abdominal recurrence was detected. The abdominal mass was resected, and radiotherapy and new chemotherapy protocol were given. The present case illustrates a rare case of primary cardiac angiosarcoma posing a diagnostic dilemma in an adolescent girl. |
format | Online Article Text |
id | pubmed-5873788 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Sociedade Brasileira de Cirurgia Cardiovascular |
record_format | MEDLINE/PubMed |
spelling | pubmed-58737882018-04-02 A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma Citak, Elvan Caglar Ozeren, Murat Karaca, M. Kerem Karpuz, Derya Karahan, Feryal Yilmaz, Eda Bengi Balci, Yuksel Kara, Pelin Ozcan Arpaci, Rabia Bozdogan Braz J Cardiovasc Surg Case Report Cardiac angiosarcomas are extremely rare in childhood, they are rapidly progressive tumours that often present themselves as diagnostic dilemmas, resulting in delayed diagnosis. Also, extracardiac manifestations, including abdominal pain, are extremely rare in patients with intracardiac tumors. We herein present the case of a 15-year-old girl who presented with abdominal pain. Echocardiography and thoracic computed tomography showed right atrial mass. The patient underwent surgery, chemotherapy, and radiotherapy. Eight months after treatment, abdominal recurrence was detected. The abdominal mass was resected, and radiotherapy and new chemotherapy protocol were given. The present case illustrates a rare case of primary cardiac angiosarcoma posing a diagnostic dilemma in an adolescent girl. Sociedade Brasileira de Cirurgia Cardiovascular 2018 /pmc/articles/PMC5873788/ /pubmed/29617509 http://dx.doi.org/10.21470/1678-9741-2017-0095 Text en http://creativecommons.org/licenses/by/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Citak, Elvan Caglar Ozeren, Murat Karaca, M. Kerem Karpuz, Derya Karahan, Feryal Yilmaz, Eda Bengi Balci, Yuksel Kara, Pelin Ozcan Arpaci, Rabia Bozdogan A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma |
title | A Rare Cause of Abdominal Pain in Childhood: Cardiac
Angiosarcoma |
title_full | A Rare Cause of Abdominal Pain in Childhood: Cardiac
Angiosarcoma |
title_fullStr | A Rare Cause of Abdominal Pain in Childhood: Cardiac
Angiosarcoma |
title_full_unstemmed | A Rare Cause of Abdominal Pain in Childhood: Cardiac
Angiosarcoma |
title_short | A Rare Cause of Abdominal Pain in Childhood: Cardiac
Angiosarcoma |
title_sort | rare cause of abdominal pain in childhood: cardiac
angiosarcoma |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5873788/ https://www.ncbi.nlm.nih.gov/pubmed/29617509 http://dx.doi.org/10.21470/1678-9741-2017-0095 |
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