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A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma

Cardiac angiosarcomas are extremely rare in childhood, they are rapidly progressive tumours that often present themselves as diagnostic dilemmas, resulting in delayed diagnosis. Also, extracardiac manifestations, including abdominal pain, are extremely rare in patients with intracardiac tumors. We h...

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Autores principales: Citak, Elvan Caglar, Ozeren, Murat, Karaca, M. Kerem, Karpuz, Derya, Karahan, Feryal, Yilmaz, Eda Bengi, Balci, Yuksel, Kara, Pelin Ozcan, Arpaci, Rabia Bozdogan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Cirurgia Cardiovascular 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5873788/
https://www.ncbi.nlm.nih.gov/pubmed/29617509
http://dx.doi.org/10.21470/1678-9741-2017-0095
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author Citak, Elvan Caglar
Ozeren, Murat
Karaca, M. Kerem
Karpuz, Derya
Karahan, Feryal
Yilmaz, Eda Bengi
Balci, Yuksel
Kara, Pelin Ozcan
Arpaci, Rabia Bozdogan
author_facet Citak, Elvan Caglar
Ozeren, Murat
Karaca, M. Kerem
Karpuz, Derya
Karahan, Feryal
Yilmaz, Eda Bengi
Balci, Yuksel
Kara, Pelin Ozcan
Arpaci, Rabia Bozdogan
author_sort Citak, Elvan Caglar
collection PubMed
description Cardiac angiosarcomas are extremely rare in childhood, they are rapidly progressive tumours that often present themselves as diagnostic dilemmas, resulting in delayed diagnosis. Also, extracardiac manifestations, including abdominal pain, are extremely rare in patients with intracardiac tumors. We herein present the case of a 15-year-old girl who presented with abdominal pain. Echocardiography and thoracic computed tomography showed right atrial mass. The patient underwent surgery, chemotherapy, and radiotherapy. Eight months after treatment, abdominal recurrence was detected. The abdominal mass was resected, and radiotherapy and new chemotherapy protocol were given. The present case illustrates a rare case of primary cardiac angiosarcoma posing a diagnostic dilemma in an adolescent girl.
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spelling pubmed-58737882018-04-02 A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma Citak, Elvan Caglar Ozeren, Murat Karaca, M. Kerem Karpuz, Derya Karahan, Feryal Yilmaz, Eda Bengi Balci, Yuksel Kara, Pelin Ozcan Arpaci, Rabia Bozdogan Braz J Cardiovasc Surg Case Report Cardiac angiosarcomas are extremely rare in childhood, they are rapidly progressive tumours that often present themselves as diagnostic dilemmas, resulting in delayed diagnosis. Also, extracardiac manifestations, including abdominal pain, are extremely rare in patients with intracardiac tumors. We herein present the case of a 15-year-old girl who presented with abdominal pain. Echocardiography and thoracic computed tomography showed right atrial mass. The patient underwent surgery, chemotherapy, and radiotherapy. Eight months after treatment, abdominal recurrence was detected. The abdominal mass was resected, and radiotherapy and new chemotherapy protocol were given. The present case illustrates a rare case of primary cardiac angiosarcoma posing a diagnostic dilemma in an adolescent girl. Sociedade Brasileira de Cirurgia Cardiovascular 2018 /pmc/articles/PMC5873788/ /pubmed/29617509 http://dx.doi.org/10.21470/1678-9741-2017-0095 Text en http://creativecommons.org/licenses/by/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Citak, Elvan Caglar
Ozeren, Murat
Karaca, M. Kerem
Karpuz, Derya
Karahan, Feryal
Yilmaz, Eda Bengi
Balci, Yuksel
Kara, Pelin Ozcan
Arpaci, Rabia Bozdogan
A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma
title A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma
title_full A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma
title_fullStr A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma
title_full_unstemmed A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma
title_short A Rare Cause of Abdominal Pain in Childhood: Cardiac Angiosarcoma
title_sort rare cause of abdominal pain in childhood: cardiac angiosarcoma
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5873788/
https://www.ncbi.nlm.nih.gov/pubmed/29617509
http://dx.doi.org/10.21470/1678-9741-2017-0095
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