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C3 glomerulopathy in cystic fibrosis: a case report
BACKGROUND: C3 glomerulonephritis is a rare glomerulopathy characterized at renal biopsy by C3 deposition, alone or with scanty immunoglobulins, as well as by an electron-dense material in mesangium, subendothelial and subepithelial space. An abnormal systemic activation of the alternative pathway o...
Autores principales: | Santoro, Domenico, Siligato, Rossella, Vadalà, Carmela, Lucanto, Mariacristina, Cristadoro, Simona, Conti, Giovanni, Buemi, Michele, Costa, Stefano, Sabadini, Ettore, Magazzù, Giuseppe |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5875003/ https://www.ncbi.nlm.nih.gov/pubmed/29592796 http://dx.doi.org/10.1186/s12882-018-0880-y |
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