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Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report

Olmsted syndrome (OS) is a rare congenital, mutilating palmoplantar keratoderma first described by Olmsted in 1927. It starts in the neonatal period or in childhood, and has a slow but progressive disabling course. We report the case of a 16-year-old boy who presented with keratoderma of the palm an...

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Autores principales: Zeeshan, Md., Jha, Abhijeet K., Chaudhary, R. K. P.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5885617/
https://www.ncbi.nlm.nih.gov/pubmed/29644198
http://dx.doi.org/10.4103/idoj.IDOJ_95_17
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author Zeeshan, Md.
Jha, Abhijeet K.
Chaudhary, R. K. P.
author_facet Zeeshan, Md.
Jha, Abhijeet K.
Chaudhary, R. K. P.
author_sort Zeeshan, Md.
collection PubMed
description Olmsted syndrome (OS) is a rare congenital, mutilating palmoplantar keratoderma first described by Olmsted in 1927. It starts in the neonatal period or in childhood, and has a slow but progressive disabling course. We report the case of a 16-year-old boy who presented with keratoderma of the palm and soles since childhood with lateral supraciliary madarosis and clubbing. The patient was started on oral retinoids and topical keratolytics and had partial improvement in 2 months. Keratoderma of the palms and soles along with lateral supraciliary madarosis and clubbing in our case is a very rare finding, and to the best of our knowledge, has not been reported so far.
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spelling pubmed-58856172018-04-11 Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report Zeeshan, Md. Jha, Abhijeet K. Chaudhary, R. K. P. Indian Dermatol Online J Case Report Olmsted syndrome (OS) is a rare congenital, mutilating palmoplantar keratoderma first described by Olmsted in 1927. It starts in the neonatal period or in childhood, and has a slow but progressive disabling course. We report the case of a 16-year-old boy who presented with keratoderma of the palm and soles since childhood with lateral supraciliary madarosis and clubbing. The patient was started on oral retinoids and topical keratolytics and had partial improvement in 2 months. Keratoderma of the palms and soles along with lateral supraciliary madarosis and clubbing in our case is a very rare finding, and to the best of our knowledge, has not been reported so far. Medknow Publications & Media Pvt Ltd 2018 /pmc/articles/PMC5885617/ /pubmed/29644198 http://dx.doi.org/10.4103/idoj.IDOJ_95_17 Text en Copyright: © 2018 Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Zeeshan, Md.
Jha, Abhijeet K.
Chaudhary, R. K. P.
Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report
title Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report
title_full Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report
title_fullStr Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report
title_full_unstemmed Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report
title_short Olmsted Syndrome with Lateral Supraciliary Madarosis and Clubbing: A Rare Case Report
title_sort olmsted syndrome with lateral supraciliary madarosis and clubbing: a rare case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5885617/
https://www.ncbi.nlm.nih.gov/pubmed/29644198
http://dx.doi.org/10.4103/idoj.IDOJ_95_17
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