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X-Linked Lymphoproliferative Disease Type 1: A Clinical and Molecular Perspective

X-linked lymphoproliferative disease (XLP) was first described in the 1970s as a fatal lymphoproliferative syndrome associated with infection with Epstein–Barr virus (EBV). Features include hemophagocytic lymphohistiocytosis (HLH), lymphomas, and dysgammaglobulinemias. Molecular cloning of the causa...

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Detalles Bibliográficos
Autores principales:	Panchal, Neelam, Booth, Claire, Cannons, Jennifer L., Schwartzberg, Pamela L.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2018
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5893764/ https://www.ncbi.nlm.nih.gov/pubmed/29670631 http://dx.doi.org/10.3389/fimmu.2018.00666

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