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ATP Synthase Diseases of Mitochondrial Genetic Origin

Devastating human neuromuscular disorders have been associated to defects in the ATP synthase. This enzyme is found in the inner mitochondrial membrane and catalyzes the last step in oxidative phosphorylation, which provides aerobic eukaryotes with ATP. With the advent of structures of complete ATP...

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Detalles Bibliográficos
Autores principales:	Dautant, Alain, Meier, Thomas, Hahn, Alexander, Tribouillard-Tanvier, Déborah, di Rago, Jean-Paul, Kucharczyk, Roza
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2018
Materias:	Physiology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5893901/ https://www.ncbi.nlm.nih.gov/pubmed/29670542 http://dx.doi.org/10.3389/fphys.2018.00329

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