Cargando…

Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa

BACKGROUND: Poland syndrome (PS) is a rare congenital anomaly associated with absent or hypoplastic pectoralis major muscle and a wide spectrum of ipsilateral thoracic and upper extremity deformities. Hidradenitis suppurativa (HS) is a recurrent inflammatory follicular disease that commonly affects...

Descripción completa

Detalles Bibliográficos
Autores principales: Goyal, Pradeep, Motiwala, Henal, Gupta, Nishant, Gupta, Sonali, Bansal, Itisha, Hooda, Kusum, Kumar, Yogesh, Olsavsky, Thomas D.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Termedia Publishing House 2017
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5894031/
https://www.ncbi.nlm.nih.gov/pubmed/29657625
http://dx.doi.org/10.12659/PJR.902677
_version_ 1783313420321292288
author Goyal, Pradeep
Motiwala, Henal
Gupta, Nishant
Gupta, Sonali
Bansal, Itisha
Hooda, Kusum
Kumar, Yogesh
Olsavsky, Thomas D.
author_facet Goyal, Pradeep
Motiwala, Henal
Gupta, Nishant
Gupta, Sonali
Bansal, Itisha
Hooda, Kusum
Kumar, Yogesh
Olsavsky, Thomas D.
author_sort Goyal, Pradeep
collection PubMed
description BACKGROUND: Poland syndrome (PS) is a rare congenital anomaly associated with absent or hypoplastic pectoralis major muscle and a wide spectrum of ipsilateral thoracic and upper extremity deformities. Hidradenitis suppurativa (HS) is a recurrent inflammatory follicular disease that commonly affects the apocrine-bearing skin and involves follicular occlusion and hyperkeratosis. CASE REPORT: We report a case of a 46-year-old male with a history of chronic recurrent hidradenitis suppurativa who was incidentally found to have a simple type of Poland syndrome with incidental hypoplasia of ipsilateral gluteal muscles. CONCLUSIONS: Not only can PS present with HS, which we describe for the first time, but it is also associated with a wide variability of symptoms such as previously unknown co-existence of gluteal muscles hypoplasia.
format Online
Article
Text
id pubmed-5894031
institution National Center for Biotechnology Information
language English
publishDate 2017
publisher Termedia Publishing House
record_format MEDLINE/PubMed
spelling pubmed-58940312018-04-13 Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa Goyal, Pradeep Motiwala, Henal Gupta, Nishant Gupta, Sonali Bansal, Itisha Hooda, Kusum Kumar, Yogesh Olsavsky, Thomas D. Pol J Radiol Case Report BACKGROUND: Poland syndrome (PS) is a rare congenital anomaly associated with absent or hypoplastic pectoralis major muscle and a wide spectrum of ipsilateral thoracic and upper extremity deformities. Hidradenitis suppurativa (HS) is a recurrent inflammatory follicular disease that commonly affects the apocrine-bearing skin and involves follicular occlusion and hyperkeratosis. CASE REPORT: We report a case of a 46-year-old male with a history of chronic recurrent hidradenitis suppurativa who was incidentally found to have a simple type of Poland syndrome with incidental hypoplasia of ipsilateral gluteal muscles. CONCLUSIONS: Not only can PS present with HS, which we describe for the first time, but it is also associated with a wide variability of symptoms such as previously unknown co-existence of gluteal muscles hypoplasia. Termedia Publishing House 2017-10-20 /pmc/articles/PMC5894031/ /pubmed/29657625 http://dx.doi.org/10.12659/PJR.902677 Text en Copyright © Polish Medical Society of Radiology 2017 https://creativecommons.org/licenses/by-nc-nd/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-Noncommercial-No Derivatives 4.0 International (CC BY-NC-ND 4.0). License allowing third parties to download articles and share them with others as long as they credit the authors and the publisher, but without permission to change them in any way or use them commercially.
spellingShingle Case Report
Goyal, Pradeep
Motiwala, Henal
Gupta, Nishant
Gupta, Sonali
Bansal, Itisha
Hooda, Kusum
Kumar, Yogesh
Olsavsky, Thomas D.
Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa
title Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa
title_full Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa
title_fullStr Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa
title_full_unstemmed Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa
title_short Poland Syndrome with Ipsilateral Hypoplasia of Gluteal Muscles and Contralateral Hidradenitis Suppurativa
title_sort poland syndrome with ipsilateral hypoplasia of gluteal muscles and contralateral hidradenitis suppurativa
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5894031/
https://www.ncbi.nlm.nih.gov/pubmed/29657625
http://dx.doi.org/10.12659/PJR.902677
work_keys_str_mv AT goyalpradeep polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa
AT motiwalahenal polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa
AT guptanishant polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa
AT guptasonali polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa
AT bansalitisha polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa
AT hoodakusum polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa
AT kumaryogesh polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa
AT olsavskythomasd polandsyndromewithipsilateralhypoplasiaofglutealmusclesandcontralateralhidradenitissuppurativa