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Photoreceptor-induced RPE phagolysosomal maturation defects in Stargardt-like Maculopathy (STGD3)
For many neurodegenerative disorders, expression of a pathological protein by one cell type impedes function of other cell types, which in turn contributes to the death of the first cell type. In transgenic mice modelling Stargardt-like (STGD3) maculopathy, human mutant ELOVL4 expression by photorec...
Autores principales: | Dejos, Camille, Kuny, Sharee, Han, Woo Hyun, Capel, Heather, Lemieux, Hélène, Sauvé, Yves |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Nature Publishing Group UK
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5899129/ https://www.ncbi.nlm.nih.gov/pubmed/29654292 http://dx.doi.org/10.1038/s41598-018-24357-4 |
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