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Primary Pleuropulmonary Synovial Sarcoma: A Case

Primary pleuropulmonary synovial sarcoma is extremely rare. The diagnosis can only be made after having eliminated an extrapleuropulmonary localization in the past and at the time of diagnosis. Our presentation is about a 40-year-old woman having a cough and dyspnea since three weeks ago; imaging ha...

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Autores principales: Mrabet, Fatima Zahra, El Ouazzani, Hafsa, El Akkari, Leila, Hammi, Sanaa, Bourkadi, Jamal Eddine, Zouaidia, Fouad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5904799/
https://www.ncbi.nlm.nih.gov/pubmed/29850352
http://dx.doi.org/10.1155/2018/5190271
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author Mrabet, Fatima Zahra
El Ouazzani, Hafsa
El Akkari, Leila
Hammi, Sanaa
Bourkadi, Jamal Eddine
Zouaidia, Fouad
author_facet Mrabet, Fatima Zahra
El Ouazzani, Hafsa
El Akkari, Leila
Hammi, Sanaa
Bourkadi, Jamal Eddine
Zouaidia, Fouad
author_sort Mrabet, Fatima Zahra
collection PubMed
description Primary pleuropulmonary synovial sarcoma is extremely rare. The diagnosis can only be made after having eliminated an extrapleuropulmonary localization in the past and at the time of diagnosis. Our presentation is about a 40-year-old woman having a cough and dyspnea since three weeks ago; imaging had showed a left pleurisy with pleuropulmonary process. Histological study of the biopsy confirmed the diagnosis of pleuropulmonary synovial sarcoma. PET-SCAN had not identified any extrathoracic localization. This tumor is known for its aggressive nature and high risk of metastasis. Its primitive character is retained following a diagnostic procedure of exclusion. Surgical treatment remains the best therapeutic tool when it is technically feasible; otherwise the prognosis is often unfortunate. In this paper, we report a case of primary pleuropulmonary synovial sarcoma. Through this case, we present a rare disease that is often difficult to diagnose.
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spelling pubmed-59047992018-05-30 Primary Pleuropulmonary Synovial Sarcoma: A Case Mrabet, Fatima Zahra El Ouazzani, Hafsa El Akkari, Leila Hammi, Sanaa Bourkadi, Jamal Eddine Zouaidia, Fouad Case Rep Pulmonol Case Report Primary pleuropulmonary synovial sarcoma is extremely rare. The diagnosis can only be made after having eliminated an extrapleuropulmonary localization in the past and at the time of diagnosis. Our presentation is about a 40-year-old woman having a cough and dyspnea since three weeks ago; imaging had showed a left pleurisy with pleuropulmonary process. Histological study of the biopsy confirmed the diagnosis of pleuropulmonary synovial sarcoma. PET-SCAN had not identified any extrathoracic localization. This tumor is known for its aggressive nature and high risk of metastasis. Its primitive character is retained following a diagnostic procedure of exclusion. Surgical treatment remains the best therapeutic tool when it is technically feasible; otherwise the prognosis is often unfortunate. In this paper, we report a case of primary pleuropulmonary synovial sarcoma. Through this case, we present a rare disease that is often difficult to diagnose. Hindawi 2018-04-04 /pmc/articles/PMC5904799/ /pubmed/29850352 http://dx.doi.org/10.1155/2018/5190271 Text en Copyright © 2018 Fatima Zahra Mrabet et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Mrabet, Fatima Zahra
El Ouazzani, Hafsa
El Akkari, Leila
Hammi, Sanaa
Bourkadi, Jamal Eddine
Zouaidia, Fouad
Primary Pleuropulmonary Synovial Sarcoma: A Case
title Primary Pleuropulmonary Synovial Sarcoma: A Case
title_full Primary Pleuropulmonary Synovial Sarcoma: A Case
title_fullStr Primary Pleuropulmonary Synovial Sarcoma: A Case
title_full_unstemmed Primary Pleuropulmonary Synovial Sarcoma: A Case
title_short Primary Pleuropulmonary Synovial Sarcoma: A Case
title_sort primary pleuropulmonary synovial sarcoma: a case
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5904799/
https://www.ncbi.nlm.nih.gov/pubmed/29850352
http://dx.doi.org/10.1155/2018/5190271
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