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Biomarkers of Myocardial Fibrosis: Revealing the Natural History of Fibrogenesis in Fabry Disease Cardiomyopathy

BACKGROUND: Cardiomyopathy is a major determinant of overall Fabry disease (FD) prognosis, with the worst outcomes in patients with myocardial fibrosis. Late gadolinium enhancement is currently the gold standard for evaluation of replacement myocardial fibrosis; however, this event is irreversible,...

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Detalles Bibliográficos
Autores principales:	Aguiar, Patrício, Azevedo, Olga, Pinto, Rui, Marino, Jacira, Cardoso, Carlos, Sousa, Nuno, Cunha, Damião, Hughes, Derralynn, Ducla Soares, José Luís
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2018
Materias:	Original Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5907540/ https://www.ncbi.nlm.nih.gov/pubmed/29535138 http://dx.doi.org/10.1161/JAHA.117.007124

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