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BMPR2 mutations and endothelial dysfunction in pulmonary arterial hypertension (2017 Grover Conference Series)

Despite the discovery more than 15 years ago that patients with hereditary pulmonary arterial hypertension (HPAH) inherit BMP type 2 receptor (BMPR2) mutations, it is still unclear how these mutations cause disease. In part, this is attributable to the rarity of HPAH and difficulty obtaining tissue...

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Detalles Bibliográficos
Autores principales:	Frump, Andrea, Prewitt, Allison, de Caestecker, Mark P.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	SAGE Publications 2018
Materias:	Review Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5912278/ https://www.ncbi.nlm.nih.gov/pubmed/29521190 http://dx.doi.org/10.1177/2045894018765840

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